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L2HGDH 抗体 (AA 1-220)

This anti-L2HGDH antibody is a 兔 多克隆 antibody detecting L2HGDH in WB 和 IF. Suitable for 人.
产品编号 ABIN7268160
发货至: 中国

Quick Overview for L2HGDH 抗体 (AA 1-220) (ABIN7268160)

抗原

See all L2HGDH 抗体
L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))

适用

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宿主

  • 32

克隆类型

  • 32
多克隆

标记

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This L2HGDH antibody is un-conjugated

应用范围

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Western Blotting (WB), Immunofluorescence (IF)
  • 抗原表位

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    AA 1-220

    原理

    L2HGDH Rabbit pAb

    序列

    MVPALRYLVG ACGRARGLFA GGSPGACGFA SGRPRPLCGG SRSASTSSFD IVIVGGGIVG LASARALILR HPSLSIGVLE KEKDLAVHQT GHNSGVIHSG IYYKPESLKA KLCVQGAALL YEYCQQKGIS YKQCGKLIVA VEQEEIPRLQ ALYEKGLQNG VPGLRLIQQE DIKKKEPYCR GLMAIDCPHT GIVDYRQVAL SFAQDFQEAG GSVLTNFEVK

    交叉反应

    人, 小鼠

    产品特性

    Polyclonal Antibodies

    纯化方法

    Affinity purification

    免疫原

    Recombinant fusion protein containing a sequence corresponding to amino acids 1-220 of human L2HGDH (NP_079160.1).

    亚型

    IgG
  • 应用备注

    WB,1:500 - 1:2000,IF,1:50 - 1:200

    限制

    仅限研究用
  • 状态

    Liquid

    缓冲液

    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

    储存液

    Sodium azide

    注意事项

    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    储存条件

    -20 °C

    储存方法

    Store at -20°C. Avoid freeze / thaw cycles.
  • 抗原

    L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))

    别名

    L2HGDH

    背景

    This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.,L2HGDH,C14orf160,L2HGA,Signal Transduction,Cell Biology & Developmental Biology,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,L2HGDH

    分子量

    48kDa/50kDa

    基因ID

    79944

    UniProt

    Q9H9P8
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