DMGDH 抗体 (C-Term)
Quick Overview for DMGDH 抗体 (C-Term) (ABIN7180160)
抗原
See all DMGDH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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交叉反应
- 人
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纯化方法
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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免疫原
- Synthesized peptide derived from C-terminal of Human DMGDH.
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亚型
- IgG
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anti-Dimethylglycine Dehydrogenase (DMGDH) (AA 429-524) antibody
DMGDH 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Dimethylglycine Dehydrogenase (DMGDH) (C-Term) antibodyDMGDH 适用: 人, 小鼠 WB, ELISA, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Dimethylglycine Dehydrogenase (DMGDH) (C-Term) antibodyDMGDH 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Dimethylglycine Dehydrogenase (DMGDH) (C-Term) antibodyDMGDH 适用: 人, 猴 WB, IHC 宿主: 兔 Polyclonal unconjugated
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应用备注
- WB:1:500-1:3000,
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150 mM NaCl, 0.02 % sodium azide and 50 % glycerol.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C,-80 °C
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储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- DMGDH (Dimethylglycine Dehydrogenase (DMGDH))
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别名
- DMGDH
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背景
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Background: This gene encodes an enzyme involved in the catabolism of choline, catalyzing the oxidative demethylation of dimethylglycine to form sarcosine. The enzyme is found as a monomer in the mitochondrial matrix, and uses flavin adenine dinucleotide and folate as cofactors. Mutation in this gene causes dimethylglycine dehydrogenase deficiency, characterized by a fishlike body odor, chronic muscle fatigue, and elevated levels of the muscle form of creatine kinase in serum. Alternative splicing results in multiple transcript variants.
Binzak B.A., Mol. Genet. Metab. 69:181-187(2000).
Binzak B.A., Am. J. Hum. Genet. 68:839-847(2001).
Moolenaar S.H., Clin. Chem. 45:459-464(1999)Aliases: Dimethylglycine dehydrogenase antibody, Dimethylglycine dehydrogenase, mitochondrial antibody, Dmgdh antibody, M2GD_HUMAN antibody, ME2GLYDH antibody, mitochondrial antibody
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UniProt
- Q9UI17
抗原
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