FUCA1 抗体 (N-Term)
Quick Overview for FUCA1 抗体 (N-Term) (ABIN633859)
抗原
See all FUCA1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- N-Term
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特异性
- FUCA1 antibody was raised against the N terminal of FUCA1
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纯化方法
- Affinity purified
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免疫原
- FUCA1 antibody was raised using the N terminal of FUCA1 corresponding to a region with amino acids PSPVSWNWNSKDVGPHRDLVGELGTALRKRNIRYGLYHSLLEWFHPLYLL
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anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 185-447) antibody
FUCA1 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 53-289) antibodyFUCA1 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 1-461) antibodyFUCA1 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) antibodyFUCA1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 321-420) antibodyFUCA1 适用: 小鼠 WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 1-461) antibodyFUCA1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 23-461) antibodyFUCA1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1D4 unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 265-294) antibodyFUCA1 适用: 人 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB19323 unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) antibodyFUCA1 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 32-158) antibodyFUCA1 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
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应用备注
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WB: 1 µg/mL
Optimal conditions should be determined by the investigator. -
说明
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FUCA1 Blocking Peptide, (ABIN5613657), is also available for use as a blocking control in assays to test for specificity of this FUCA1 antibody
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限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Lyophilized powder. Add distilled water for a 1 mg/mL concentration of FUCA1 antibody in PBS
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浓度
- Lot specific
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缓冲液
- PBS
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注意事项
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Avoid repeated freeze/thaw cycles.
Dilute only prior to immediate use. -
储存条件
- 4 °C/-20 °C
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储存方法
- Store at 2-8 °C for short periods. For longer periods of storage, store at -20 °C.
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- FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))
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别名
- FUCA1
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背景
- Alpha-L-fucosidase (EC 3.2.1.51) is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. At least 2 separate polymorphic alpha-L-fucosidases are recognised in man: that in tissues, FUCA1, which is deficient in fucosidosis, and that in plasma, FUCA2. Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form, coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form, and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.
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分子量
- 54 kDa (MW of target protein)
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途径
- Glycosaminoglycan Metabolic Process
抗原
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