L2HGDH 抗体
Quick Overview for L2HGDH 抗体 (ABIN6293250)
抗原
See all L2HGDH 抗体适用
宿主
克隆类型
标记
应用范围
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纯化方法
- Affinity purification
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免疫原
- Recombinant protein of human L2HGDH
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亚型
- IgG
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应用备注
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WB 1:500 - 1:2000
IF 1:50 - 1:200 -
说明
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Widely expressed, Highly expressed in brain, testis and muscle, Expressed to a lower extent in lymphocytes, fibroblasts, keratinocytes, placenta, bladder, small intestine, liver and bone marrow
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限制
- 仅限研究用
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缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20C. Avoid freeze / thaw cycles.
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- L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
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别名
- L2HGDH
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背景
- This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.
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分子量
- 50.316 kDa
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基因ID
- 79944
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UniProt
- Q9H9P8
抗原
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