Dysferlin 抗体 (AA 1901-2119) (AbBy Fluor® 750)
Quick Overview for Dysferlin 抗体 (AA 1901-2119) (AbBy Fluor® 750) (ABIN5001602)
抗原
See all Dysferlin (DYSF) 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1901-2119
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交叉反应
- 人
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预测反应
- Mouse,Rat,Dog,Cow,Pig,Horse,Rabbit,Guinea Pig
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纯化方法
- Purified by Protein A.
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免疫原
- KLH conjugated synthetic peptide derived from human DYSF
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亚型
- IgG
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anti-Dysferlin (DYSF) (AA 105-278) antibody
DYSF 适用: 人 ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (C-Term) antibodyDYSF 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) antibodyDYSF 适用: 人 WB, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (AA 1584-1633) antibodyDYSF 适用: 人, 小鼠, 豚鼠, 兔, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (AA 215-264) antibodyDYSF 适用: 人, Cow, 犬, 豚鼠, 兔, Pig, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (AA 1999-2016) antibodyDYSF 适用: 人 IHC, IHC (p), IHC (fro) 宿主: 小鼠 Monoclonal Ham1-7B6 unconjugated
anti-Dysferlin (DYSF) (AA 1-479) antibodyDYSF 适用: 人 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (C-Term) antibodyDYSF 适用: 人, 小鼠, 大鼠, Cow, 犬, Pig WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Dysferlin (DYSF) (Middle Region) antibodyDYSF 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 兔, 马, 斑马鱼 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- FCM 1:20-100
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 μg/μL
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缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
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有效期
- 12 months
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- Dysferlin (DYSF)
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别名
- Dysferlin
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背景
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Synonyms: DMAT, DYSF, Dysferlin Dystrophy associated fer 1 like protein Fer 1 like protein 1, Dysferlin limb girdle muscular dystrophy 2B autosomal recessive, Dysferlin limb girdle muscular dystrophy 2B, Dystrophy associated fer 1 like 1, Dystrophy associated fer 1 like protein, Dystrophy associated fer1 like 1, Dystrophy associated fer1 like protein, Fer 1 like protein 1, Fer1 like protein 1, FER1L1, FLJ00175, FLJ90168, LGMD 2B, LGMD2B, Limb girdle muscular dystrophy 2B autosomal recessive , Limb girdle muscular dystrophy 2B, Miyoshi myopathy, MM, DYSF_HUMAN.
Background: The protein encoded by this gene belongs to the ferlin family and is a skeletal muscle protein found associated with the sarcolemma. It is involved in muscle contraction and contains C2 domains that play a role in calcium-mediated membrane fusion events, suggesting that it may be involved in membrane regeneration and repair. In addition, the protein encoded by this gene binds caveolin-3, a skeletal muscle membrane protein which is important in the formation of caveolae. Specific mutations in this gene have been shown to cause autosomal recessive limb girdle muscular dystrophy type 2B (LGMD2B) as well as Miyoshi myopathy. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2008].
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基因ID
- 8291
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UniProt
- O75923
抗原
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