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Dysferlin 抗体

DYSF 适用: 人 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7181039
发货至: 中国
  • 抗原 See all Dysferlin (DYSF) 抗体
    Dysferlin (DYSF)
    适用
    • 53
    • 24
    • 5
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    • 5
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    • 2
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    • 1
    宿主
    • 49
    • 3
    • 1
    克隆类型
    • 40
    • 13
    多克隆
    标记
    • 20
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    This Dysferlin antibody is un-conjugated
    应用范围
    • 14
    • 14
    • 13
    • 9
    • 6
    • 3
    • 1
    • 1
    • 1
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    Western Blotting (WB), ELISA
    交叉反应
    人, 小鼠
    纯化方法
    The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
    免疫原
    Synthesized peptide derived from Human Dysferlin.
    亚型
    IgG
    Top Product
    Discover our top product DYSF Primary Antibody
  • 应用备注
    WB:1:500-1:3000,
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150 mM NaCl, 0.02 % sodium azide and 50 % glycerol.
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C,-80 °C
    储存方法
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 抗原
    Dysferlin (DYSF)
    别名
    DYSF (DYSF 产品)
    别名
    DYSF antibody, fb73b05 antibody, wu:fb73b05 antibody, si:rp71-50c18.1 antibody, DKFZp459E1226 antibody, 2310004N10Rik antibody, AI604795 antibody, D6Pas3 antibody, mFLJ00175 antibody, FER1L1 antibody, LGMD2B antibody, MMD1 antibody, dysferlin antibody, dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive) antibody, myoferlin antibody, DYSF antibody, dysf antibody, LOC589501 antibody, Dysf antibody
    背景

    Background: Key calcium ion sensor involved in the Ca2+-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress By similarity.

    Delia J. Hern?ez-Deviez, Hum. Mol. Genet., Jan 2006, 15: 129 - 142.
    Yanchao Huang, FASEB J, Mar 2007, 21: 732 - 742.
    Mengfatt Ho, Hum. Mol. Genet., Sep 2004, 13: 1999 - 2010.
    Eriko Fujita, Hum. Mol. Genet., Mar 2007, 16: 618 - 629.

    Aliases: DMAT antibody, DYSF antibody, DYSF_HUMAN antibody, Dysferlin antibody, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Dysferlin limb girdle muscular dystrophy 2B antibody, Dystrophy associated fer 1 like 1 antibody, Dystrophy associated fer 1 like protein antibody, Dystrophy associated fer1 like 1 antibody, Dystrophy associated fer1 like protein antibody, Dystrophy-associated fer-1-like protein antibody, Fer 1 like protein 1 antibody, Fer-1-like protein 1 antibody, Fer1 like protein 1 antibody, FER1L1 antibody, FLJ00175 antibody, FLJ90168 antibody, LGMD 2B antibody, LGMD2B antibody, Limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Limb girdle muscular dystrophy 2B antibody, Miyoshi myopathy antibody, MM antibody, MMD1 antibody

    UniProt
    O75923
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