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GNS 抗体 (Middle Region)

This anti-GNS antibody is a 兔 多克隆 antibody detecting GNS in WB 和 EIA. Suitable for 人.
产品编号 ABIN453065
发货至: 中国

Quick Overview for GNS 抗体 (Middle Region) (ABIN453065)

抗原

See all GNS 抗体
GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

适用

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  • 1

宿主

  • 29
  • 3
  • 1

克隆类型

  • 32
  • 1
多克隆

标记

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This GNS antibody is un-conjugated

应用范围

  • 16
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  • 2
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  • 1
Western Blotting (WB), Enzyme Immunoassay (EIA)
  • 抗原表位

    • 15
    • 3
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    Middle Region

    特异性

    This antibody detects GNS at Center, N189.

    交叉反应 (详细)

    Species reactivity (tested):Human

    纯化方法

    Prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS

    免疫原

    KLH conjugated synthetic peptide selected from the Center region of human GNS
  • 应用备注

    Western blot: 1: 50 - 1: 100. ELISA: 1: 1,000.
    Other applications not tested.
    Optimal dilutions are dependent on conditions and should be determined by the user.

    限制

    仅限研究用
  • 状态

    Liquid

    浓度

    0.25 mg/mL

    缓冲液

    PBS with 0.09 % (W/V) sodium azide

    储存液

    Sodium azide

    注意事项

    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    注意事项

    Avoid repeated freezing and thawing.

    储存条件

    4 °C/-20 °C

    储存方法

    Store the antibody at 2 - 8 °C up to one month or (in aliquots) at -20 °C for longer.
  • 抗原

    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

    别名

    GNS / G6S

    背景

    GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.Synonyms: Glucosamine-6-sulfatase, N-acetylglucosamine-6-sulfatase

    分子量

    62082 Da

    基因ID

    2799

    NCBI登录号

    NP_002067

    UniProt

    P15586

    途径

    Glycosaminoglycan Metabolic Process
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