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GNS 抗体 (AA 283-313)

This anti-GNS antibody is a 兔 多克隆 antibody detecting GNS in WB, IHC (p) 和 FACS. Suitable for 人.
产品编号 ABIN2840852
发货至: 中国

Quick Overview for GNS 抗体 (AA 283-313) (ABIN2840852)

抗原

See all GNS 抗体
GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

适用

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宿主

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  • 1

克隆类型

  • 33
  • 1
多克隆

标记

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This GNS antibody is un-conjugated

应用范围

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Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Flow Cytometry (FACS)

克隆位点

RB19341
  • 抗原表位

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    AA 283-313

    纯化方法

    This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.

    免疫原

    This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 283-313 amino acids from the Central region of human GNS.

    亚型

    Ig Fraction
  • 应用备注

    WB: 1:1000. IHC-P: 1:50~100. FC: 1:10~50

    限制

    仅限研究用
  • 状态

    Liquid

    缓冲液

    Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

    储存液

    Sodium azide

    注意事项

    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    储存条件

    4 °C,-20 °C

    储存方法

    Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.

    有效期

    6 months
  • 抗原

    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

    别名

    GNS

    背景

    GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

    分子量

    62082

    基因ID

    2799

    NCBI登录号

    NP_002067

    UniProt

    P15586

    途径

    Glycosaminoglycan Metabolic Process
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