BCKDHB 抗体 (N-Term)
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北京 101111
Quick Overview for BCKDHB 抗体 (N-Term) (ABIN2787755)
抗原
See all BCKDHB 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- N-Term
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原理
- BCKDHB Antibody - N-terminal region
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序列
- GFLHPAATVE DAAQRRQVAH FTFQPDPEPR EYGQTQKMNL FQSVTSALDN
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预测反应
- Cow: 93%, Dog: 93%, Horse: 93%, Human: 100%, Pig: 86%, Rabbit: 93%, Rat: 79%
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产品特性
- This is a rabbit polyclonal antibody against BCKDHB. It was validated on Western Blot.
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纯化方法
- Affinity Purified
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免疫原
- The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB
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anti-Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB) (AA 41-70), (N-Term) antibody
BCKDHB 适用: 人 WB, FACS, IF, IHC (p) 宿主: 兔 Polyclonal RB20925 unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB) (AA 44-74), (N-Term) antibodyBCKDHB 适用: 人 WB, FACS, IF, IHC (p), EIA 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilution should be determined by the investigator.
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说明
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP58593-100UG
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.5 mg/mL
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缓冲液
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- prevent freeze-thaw cycles
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储存条件
- 4 °C,-20 °C
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储存方法
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
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别名
- BCKDHB
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背景
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Background Information: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform.
Gene Name: branched chain keto acid dehydrogenase E1, beta polypeptide
Alternative Symbols: E1B, BCKDE1B, BCKDH E1-beta
Protein Name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial Ensembl ENSP00000443564 Ensembl ENSP00000358775
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分子量
- 23kDa
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基因ID
- 594
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UniProt
- Q5T2J3
抗原
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