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FUCA1 抗体 (N-Term)

This anti-FUCA1 antibody is a 兔 多克隆 antibody detecting FUCA1 in WB. Suitable for 人, 小鼠, 大鼠, Cow, 犬, 兔, 豚鼠, 马 和 Pig.
产品编号 ABIN2785639
发货至: 中国

Quick Overview for FUCA1 抗体 (N-Term) (ABIN2785639)

抗原

See all FUCA1 抗体
FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))

适用

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人, 小鼠, 大鼠, Cow, 犬, 兔, 豚鼠, 马, Pig

宿主

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克隆类型

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多克隆

标记

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This FUCA1 antibody is un-conjugated

应用范围

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Western Blotting (WB)
  • 抗原表位

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    N-Term

    序列

    PSPVSWNWNS KDVGPHRDLV GELGTALRKR NIRYGLYHSL LEWFHPLYLL

    预测反应

    Cow: 100%, Dog: 93%, Guinea Pig: 93%, Horse: 93%, Human: 100%, Mouse: 100%, Pig: 100%, Rabbit: 79%, Rat: 100%

    产品特性

    This is a rabbit polyclonal antibody against FUCA1. It was validated on Western Blot using a cell lysate as a positive control.

    纯化方法

    Affinity Purified

    免疫原

    The immunogen is a synthetic peptide directed towards the N terminal region of human FUCA1
  • 应用备注

    Optimal working dilutions should be determined experimentally by the investigator.

    说明

    Antigen size: 466 AA

    限制

    仅限研究用
  • 状态

    Liquid

    浓度

    Lot specific

    缓冲液

    Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

    储存液

    Sodium azide

    注意事项

    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    注意事项

    Avoid repeated freeze-thaw cycles.

    储存条件

    -20 °C

    储存方法

    For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
  • 抗原

    FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))

    别名

    FUCA1

    背景

    Alpha-L-fucosidase (EC 3.2.1.51) is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. At least 2 separate polymorphic alpha-L-fucosidases are recognized in man: that in tissues, FUCA1, which is deficient in fucosidosis, and that in plasma, FUCA2. Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form, coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form, and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.[supplied by OMIM]. Publication Note: This RefSeq record includes a subset of the publications that are available for this gene. Please see the Entrez Gene record to access additional publications.
    Alias Symbols: FUCA
    Protein Interaction Partner: PAXIP1, BARD1, APP, CUL3, VAV2, USP21, MARK2,
    Protein Size: 466

    分子量

    54 kDa

    基因ID

    2517

    NCBI登录号

    NM_000147, NP_000138

    UniProt

    P04066

    途径

    Glycosaminoglycan Metabolic Process
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