GNS 抗体 (C-Term)
Quick Overview for GNS 抗体 (C-Term) (ABIN2782155)
抗原
See all GNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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序列
- PILRGASNLT WRSDVLVEYQ GEGRNVTDPT CPSLSPGVSQ CFPDCVCEDA
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预测反应
- Cow: 100%, Dog: 93%, Goat: 100%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 100%, Rabbit: 100%, Rat: 100%, Zebrafish: 85%
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产品特性
- This is a rabbit polyclonal antibody against GNS. It was validated on Western Blot using a cell lysate as a positive control.
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纯化方法
- Affinity Purified
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免疫原
- The immunogen is a synthetic peptide directed towards the C terminal region of human GNS
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anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibody
GNS 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 283-313) antibodyGNS 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB19341 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) antibodyGNS 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 312-361) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 398-447) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 斑马鱼, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (C-Term) antibodyGNS 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 238-355) antibodyGNS 适用: 人, 小鼠, 大鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilutions should be determined experimentally by the investigator.
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说明
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Antigen size: 552 AA
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- Lot specific
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缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid repeated freeze-thaw cycles.
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储存条件
- -20 °C
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储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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别名
- GNS
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背景
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GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Alias Symbols: G6S, MGC21274
Protein Interaction Partner: LDHAL6B, BCCIP, UBFD1, CNDP2, SCLY, C11orf58, GDA, KYNU, RPS6KA1, PEPD, MVD, GLS, GLA, GBP2, G6PD, EIF5A, CASP7, CAPN1, FBXO6, UBC,
Protein Size: 552 -
分子量
- 62 kDa
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基因ID
- 2799
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NCBI登录号
- NM_002076, NP_002067
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UniProt
- P15586
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途径
- Glycosaminoglycan Metabolic Process
抗原
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