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AGL 抗体

(Amylo-alpha-1, 6-Glucosidase, 4-alpha-Glucanotransferase (AGL))
This gene encodes the glycogen debrancher enzyme which is involved in glycogen degradation. This enzyme has two independent catalytic activities which occur at different sites on the protein: a 4-alpha-glucotransferase activity and a amylo-1,6-glucosidase activity. Mutations in this gene are associated with glycogen storage disease although a wide range of enzymatic and clinical variability occurs which may be due to tissue-specific alternative splicing. Alternatively spliced transcripts encoding different isoforms have been described. [provided by RefSeq, Jul 2008].

41 results :

AGL 适用: 人 WB, IF 宿主: 兔 Polyclonal RB4978 unconjugated
Pubmed 6 references
产品编号 ABIN389030
 
AGL 适用: 人 WB, IF 宿主: 兔 Polyclonal RB4976 unconjugated
Pubmed 10 references
产品编号 ABIN1882062
 
AGL 适用: 人 WB, IF 宿主: 兔 Polyclonal RB5106 unconjugated
产品编号 ABIN6243594
 
AGL 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN513178
 
AGL 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7001167
 
AGL 适用: 人 ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7154202
 
AGL 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6136632
 
AGL 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN4902856
 
KD Validated AGL 适用: 人, 小鼠, 大鼠 WB, IF, IHC, ICC, FACS 宿主: 兔 Monoclonal unconjugated Recombinant Antibody
产品编号 ABIN7606830
 
AGL 适用: 人 WB, IF, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN357688
 
AGL 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7154205
 
AGL 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7154203
 
AGL 适用: 人 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7634518
 
AGL 适用: 小鼠 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7634519
 
AGL 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7154204
 
AGL 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1841449
 
AGL 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN2615039
 
AGL 适用: 人 WB, ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2615042
 
AGL 适用: 人 ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2615041
 
AGL 适用: 人 ELISA, IF, ICC 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1891929
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunofluorescence (IF)
    • ELISA
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (IHC)
    • Immunoprecipitation (IP)
    • Flow Cytometry (FACS)
    • Enzyme Immunoassay (EIA)
    • Immunofluorescence (fixed cells) (IF/ICC)
  • 适用
    • Human
    • Mouse
    • Rat
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 27A59
    • RB4976
    • RB4978
    • RB5106
  • 抗原表位
    • AA 1479-1510
    • N-Term
    • AA 1217-1378
    • C-Term
    • AA 1-1532
    • AA 1487-1516
    • AA 1167-1532
    • AA 1197-1532
    • AA 1233-1532
    • AA 3-265
    • AA 357-387
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • APC
    • PE
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
  • 抗体亚型
    • IgG
    • Ig Fraction
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • KD Validated
  • Supplier
    • antibodies-online
    • Signalway
    • Abcepta
    • Biomatik
    • Boster Bio
    • Abbexa
    • Acris
    • St John's Laboratory
    • USBio

Latest Publications for our AGL 抗体

Trump et al.: "Commentary on: "Enzalutamide monotherapy in hormone-naive prostate cancer: primary analysis of an open-label, single-arm, phase 2 study." Tombal B, Borre M, Rathenborg P, Werbrouck P, Van Poppel H, ..." in: Urologic oncology, (2015) (PubMed).

Irimia, Tagliabracci, Meyer, Segvich, DePaoli-Roach, Roach: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." in: The Journal of biological chemistry, (2015) (PubMed).

Guin, Ru, Agarwal, Ritterson Lew, Owens, Comi, Theodorescu: "Loss of glycogen debranching enzyme AGL drives bladder tumor growth via induction of hyaluronic acid synthesis." in: Clinical cancer research : an official journal of the American Association for Cancer Research, (2015) (PubMed).

Liu, Zeng, Ma, Baba, Zheng, Liu, Wang: "Laforin-malin complex degrades polyglucosan bodies in concert with glycogen debranching enzyme and brain isoform glycogen phosphorylase." in: Molecular neurobiology, Vol. 49, Issue 2, pp. 645-57, (2014) (PubMed).

Zhu, Shen, Zhu, Coorey, Nguyen, Barthelmes, Gillies: "Anti-retinal antibodies in patients with macular telangiectasia type 2." in: Investigative ophthalmology & visual science, Vol. 54, Issue 8, pp. 5675-83, (2013) (PubMed).

DePaoli-Roach, Tagliabracci, Segvich, Meyer, Irimia, Roach: "Genetic depletion of the malin E3 ubiquitin ligase in mice leads to lafora bodies and the accumulation of insoluble laforin." in: The Journal of biological chemistry, Vol. 285, Issue 33, pp. 25372-81, (2010) (PubMed).

Parker, Kong, Walsh, Salajegheh, Moghadaszadeh, Amato, Nazareno, Lin, Krastins, Sarracino, Beggs, Pinkus, Greenberg: "Fast-twitch sarcomeric and glycolytic enzyme protein loss in inclusion body myositis." in: Muscle & nerve, Vol. 39, Issue 6, pp. 739-53, (2009) (PubMed).

Tagliabracci, Girard, Segvich, Meyer, Turnbull, Zhao, Minassian, Depaoli-Roach, Roach: "Abnormal metabolism of glycogen phosphate as a cause for Lafora disease." in: The Journal of biological chemistry, Vol. 283, Issue 49, pp. 33816-25, (2008) (PubMed).

Cheng, Zhang, Gentry, Worby, Dixon, Saltiel: "A role for AGL ubiquitination in the glycogen storage disorders of Lafora and Cori's disease." in: Genes & development, Vol. 21, Issue 19, pp. 2399-409, (2007) (PubMed).

Horinishi, Okubo, Tang, Hui, To, Mabuchi, Okada, Mabuchi, Murase: "Mutational and haplotype analysis of AGL in patients with glycogen storage disease type III." in: Journal of human genetics, Vol. 47, Issue 2, pp. 55-9, (2002) (PubMed).

Aliases for AGL 抗体

amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL) 抗体
glycogen debranching enzyme (agl) 抗体
glycogen debranching protein (MMAH_RS03870) 抗体
amylo-1,6-glucosidase, 4-alpha-glucanotransferase (Agl) 抗体
amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (Agl) 抗体
1110061O17Rik 抗体
9430004C13Rik 抗体
9630046L06Rik 抗体
AI850929 抗体
C77197 抗体
DDBDRAFT_0219237 抗体
DDBDRAFT_0234114 抗体
DDB_0219237 抗体
DDB_0234114 抗体
GDE 抗体
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