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Adenylosuccinate Lyase 抗体

(Adenylosuccinate Lyase (ADSL))
Adenylsuccinate lyase is involved in both de novo synthesis of purines and formation of adenosine monophosphate from inosine monophosphate. It catalyzes two reactions in AMP biosynthesis: the removal of a fumarate from succinylaminoimidazole carboxamide (SAICA) ribotide to give aminoimidazole carboxamide ribotide (AICA) and removal of fumarate from adenylosuccinate to give AMP. Adenylosuccinase deficiency results in succinylpurinemic autism, psychomotor retardation, and , in some cases, growth retardation associated with muscle wasting and epilepsy. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008].

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  • 抗原: Adenylosuccinate Lyase (ADSL)
  • Primary
Catalog no. 产品 适用 宿主 / 克隆类型 应用 价格和交货时间
ABIN6833424
Adenylosuccinate Lyase 抗体 (Alexa Fluor 594) ADSL · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN5566802
Adenylosuccinate Lyase 抗体 (AA 1-484) (APC) ADSL · Primary Antibody 人 兔 Polyclonal
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
  • 150 μg
发货至: 中国
ABIN5566801
Adenylosuccinate Lyase 抗体 (AA 1-484) ADSL · Primary Antibody 人 兔 Polyclonal
  • EIA (Enzyme Immunoassay: 所列应用)
  • RIA (Radioimmunoassay: 所列应用)
  • 150 μg
发货至: 中国
ABIN5566804
Adenylosuccinate Lyase 抗体 (AA 1-484) (FITC) ADSL · Primary Antibody 人 兔 Polyclonal
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
  • 150 μg
发货至: 中国
ABIN5566803
Adenylosuccinate Lyase 抗体 (AA 1-484) (Biotin) ADSL · Primary Antibody 人 兔 Polyclonal
  • EIA (Enzyme Immunoassay: 所列应用)
  • RIA (Radioimmunoassay: 所列应用)
  • 150 μg
发货至: 中国
ABIN5566806
Adenylosuccinate Lyase 抗体 (AA 1-484) (PE) ADSL · Primary Antibody 人 兔 Polyclonal
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
  • 150 μg
发货至: 中国
ABIN5566805
Adenylosuccinate Lyase 抗体 (AA 1-484) (PerCP) ADSL · Primary Antibody 人 兔 Polyclonal
  • FACS (Flow Cytometry: 所列应用)
  • 150 μg
发货至: 中国
ABIN8119605
Adenylosuccinate Lyase 抗体 ADSL · Primary Antibody 人, 小鼠 兔 Polyclonal
  • WB (Western Blotting: 所列应用)
  • 50 μL
发货至: 中国
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 594
产品编号 ABIN6833424
Primary Antibody
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
APC
抗原表位
AA 1-484
产品编号 ABIN5566802
Primary Antibody
  • EIA (Enzyme Immunoassay: 所列应用)
  • RIA (Radioimmunoassay: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
unconjugated
抗原表位
AA 1-484
产品编号 ABIN5566801
Primary Antibody
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
FITC
抗原表位
AA 1-484
产品编号 ABIN5566804
Primary Antibody
  • EIA (Enzyme Immunoassay: 所列应用)
  • RIA (Radioimmunoassay: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Biotin
抗原表位
AA 1-484
产品编号 ABIN5566803
Primary Antibody
  • IHC (Immunohistochemistry: 所列应用)
  • IF (Immunofluorescence: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • ICC (Immunocytochemistry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
PE
抗原表位
AA 1-484
产品编号 ABIN5566806
Primary Antibody
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
PerCP
抗原表位
AA 1-484
产品编号 ABIN5566805
Primary Antibody
  • WB (Western Blotting: 所列应用)
适用
人, 小鼠
宿主
兔
克隆形成能力
Polyclonal
标记
unconjugated
抗体亚型
IgG
产品编号 ABIN8119605

Latest Publications for our Adenylosuccinate Lyase 抗体

van Straten, van Steenbeek, Grinwis, Favier, Kummeling, van Gils, Fieten, Groot Koerkamp, Holstege, Rothuizen, Spee: "Aberrant expression and distribution of enzymes of the urea cycle and other ammonia metabolizing pathways in dogs with congenital portosystemic shunts." in: PLoS ONE, Vol. 9, Issue 6, pp. e100077, (2014) (PubMed).

Baresova, Skopova, Sikora, Patterson, Sovova, Zikanova, Kmoch: "Mutations of ATIC and ADSL affect purinosome assembly in cultured skin fibroblasts from patients with AICA-ribosiduria and ADSL deficiency." in: Human molecular genetics, Vol. 21, Issue 7, pp. 1534-43, (2012) (PubMed).

Stadler, Hjelmare, Neumann, Jonasson, Pepperkok, Uhlén, Lundberg: "Systematic validation of antibody binding and protein subcellular localization using siRNA and confocal microscopy." in: Journal of proteomics, Vol. 75, Issue 7, pp. 2236-51, (2012) (PubMed).

Blumstein, Faundez, Nakatsu, Saito, Ohno, Kelly: "The neuronal form of adaptor protein-3 is required for synaptic vesicle formation from endosomes." in: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 21, Issue 20, pp. 8034-42, (2001) (PubMed).

Zhen, Jiang, Feng, Bright, Peden, Seymour, Novak, Elliott, Gorin, Robinson, Swank: "Abnormal expression and subcellular distribution of subunit proteins of the AP-3 adaptor complex lead to platelet storage pool deficiency in the pearl mouse." in: Blood, Vol. 94, Issue 1, pp. 146-55, (1999) (PubMed).

Ooi, Moreira, DellAngelica, Poy, Wassarman, Bonifacino: "Altered expression of a novel adaptin leads to defective pigment granule biogenesis in the Drosophila eye color mutant garnet." in: The EMBO journal, Vol. 16, Issue 15, pp. 4508-18, (1997) (PubMed).

Aliases for Adenylosuccinate Lyase 抗体

adenylosuccinate lyase (ADSL) 抗体
adenylosuccinate lyase (adsl) 抗体
adenylosuccinate lyase L homeolog (adsl.L) 抗体
adenylosuccinate lyase (ASL) 抗体
adenylosuccinate lyase (purB) 抗体
adenylosuccinase; ASL (purB) 抗体
adenylosuccinate lyase (purB,adsL) 抗体
adenylosuccinate lyase (Mrub_2293) 抗体
adenylosuccinate lyase (MMAH_RS02975) 抗体
adenylosuccinate lyase (Arnit_0089) 抗体
adenylosuccinate lyase (Mesil_1058) 抗体
adenylosuccinate lyase (Slip_0597) 抗体
adenylosuccinate lyase (Trad_2452) 抗体
adenylosuccinate lyase (Deba_0652) 抗体
adenylosuccinate lyase (Toce_1174) 抗体
Adenylosuccinate lyase (Acear_2324) 抗体
Adenylosuccinate lyase (Igag_0272) 抗体
adenylosuccinate lyase (Saut_2156) 抗体
Adenylosuccinate lyase (Fbal_1996) 抗体
adenylosuccinate lyase (Ndas_2434) 抗体
adenylosuccinate lyase (Ilyop_0196) 抗体
adenylosuccinate lyase (Lbys_2961) 抗体
adenylosuccinate lyase (MFER_RS02920) 抗体
adenylosuccinate lyase (Palpr_2192) 抗体
adenylosuccinate lyase (Calni_0061) 抗体
adenylosuccinate lyase (Ftrac_3746) 抗体
L-Aspartase-like family protein (AT1G36280) 抗体
Adenylosuccinate lyase (Olsu_1764) 抗体
adenylosuccinate lyase (Adsl) 抗体
Adl 抗体
adsL 抗体
AMPS 抗体
ASASE 抗体
ASL 抗体
Asl 抗体
F15C21.8 抗体
F15C21_8 抗体
fi60b04 抗体
MGC53383 抗体
MGC69239 抗体
purB 抗体
wu:fi60b04 抗体
zgc:56061 抗体
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