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Adenylosuccinate Lyase 抗体

(Adenylosuccinate Lyase (ADSL))
Adenylsuccinate lyase is involved in both de novo synthesis of purines and formation of adenosine monophosphate from inosine monophosphate. It catalyzes two reactions in AMP biosynthesis: the removal of a fumarate from succinylaminoimidazole carboxamide (SAICA) ribotide to give aminoimidazole carboxamide ribotide (AICA) and removal of fumarate from adenylosuccinate to give AMP. Adenylosuccinase deficiency results in succinylpurinemic autism, psychomotor retardation, and , in some cases, growth retardation associated with muscle wasting and epilepsy. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008].

48 results

ADSL 适用: 人 宿主: 兔 Polyclonal Alexa Fluor 647
产品编号 ABIN6916354
100 μL
发货至: 中国
获取报价
 
ADSL 适用: 人 宿主: 兔 Polyclonal Alexa Fluor 680
产品编号 ABIN6905803
100 μL
发货至: 中国
获取报价
 
ADSL 适用: 人 宿主: 兔 Polyclonal Alexa Fluor 750
产品编号 ABIN6857613
100 μL
发货至: 中国
获取报价
 
ADSL 适用: 人 宿主: 兔 Polyclonal Alexa Fluor 594
产品编号 ABIN6833424
100 μL
发货至: 中国
获取报价
 
ADSL 适用: 人 IHC, IF, FACS, ICC 宿主: 兔 Polyclonal PE
产品编号 ABIN5566806
150 μg
发货至: 中国
获取报价
 
ADSL 适用: 人 IHC, IF, FACS, ICC 宿主: 兔 Polyclonal FITC
产品编号 ABIN5566804
150 μg
发货至: 中国
获取报价
 
ADSL 适用: 人 IHC, IF, FACS, ICC 宿主: 兔 Polyclonal APC
产品编号 ABIN5566802
150 μg
发货至: 中国
获取报价
 
ADSL 适用: 人 FACS 宿主: 兔 Polyclonal PerCP
产品编号 ABIN5566805
150 μg
发货至: 中国
获取报价
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (IHC)
    • ELISA
    • Flow Cytometry (FACS)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Enzyme Immunoassay (EIA)
    • Immunoprecipitation (IP)
    • Radioimmunoassay (RIA)
    • Immunochromatography (IC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Dog
    • Guinea Pig
    • Horse
    • Monkey
    • Cow
    • Pig
    • Rabbit
    • Sheep
  • 论文引用
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 25GB595
    • 2D10
    • AT16C10
  • 抗原表位
    • AA 185-280
    • AA 1-484
    • AA 1-310
    • AA 146-484
    • AA 188-237
    • AA 200-250
    • AA 202-441
    • Middle Region
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • APC
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
    • HRP
    • PE
    • PerCP
  • 抗体亚型
    • IgG
    • IgG1
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • KD Validated
  • Supplier
    • antibodies-online
    • Assaypro
    • Signalway
    • Abbexa
    • Aviva Systems Biology
    • Cohesion Biosciences
    • Enogene Biotech
    • OriGene
    • ProteoGenix

Latest Publications for our Adenylosuccinate Lyase 抗体

van Straten, van Steenbeek, Grinwis, Favier, Kummeling, van Gils, Fieten, Groot Koerkamp, Holstege, Rothuizen, Spee: "Aberrant expression and distribution of enzymes of the urea cycle and other ammonia metabolizing pathways in dogs with congenital portosystemic shunts." in: PLoS ONE, Vol. 9, Issue 6, pp. e100077, (2014) (PubMed).

Baresova, Skopova, Sikora, Patterson, Sovova, Zikanova, Kmoch: "Mutations of ATIC and ADSL affect purinosome assembly in cultured skin fibroblasts from patients with AICA-ribosiduria and ADSL deficiency." in: Human molecular genetics, Vol. 21, Issue 7, pp. 1534-43, (2012) (PubMed).

Stadler, Hjelmare, Neumann, Jonasson, Pepperkok, Uhlén, Lundberg: "Systematic validation of antibody binding and protein subcellular localization using siRNA and confocal microscopy." in: Journal of proteomics, Vol. 75, Issue 7, pp. 2236-51, (2012) (PubMed).

Blumstein, Faundez, Nakatsu, Saito, Ohno, Kelly: "The neuronal form of adaptor protein-3 is required for synaptic vesicle formation from endosomes." in: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 21, Issue 20, pp. 8034-42, (2001) (PubMed).

Zhen, Jiang, Feng, Bright, Peden, Seymour, Novak, Elliott, Gorin, Robinson, Swank: "Abnormal expression and subcellular distribution of subunit proteins of the AP-3 adaptor complex lead to platelet storage pool deficiency in the pearl mouse." in: Blood, Vol. 94, Issue 1, pp. 146-55, (1999) (PubMed).

Ooi, Moreira, DellAngelica, Poy, Wassarman, Bonifacino: "Altered expression of a novel adaptin leads to defective pigment granule biogenesis in the Drosophila eye color mutant garnet." in: The EMBO journal, Vol. 16, Issue 15, pp. 4508-18, (1997) (PubMed).

Aliases for Adenylosuccinate Lyase 抗体

adenylosuccinate lyase (ADSL) 抗体
adenylosuccinate lyase (adsl) 抗体
adenylosuccinate lyase L homeolog (adsl.L) 抗体
adenylosuccinate lyase (ASL) 抗体
adenylosuccinate lyase (purB) 抗体
adenylosuccinase; ASL (purB) 抗体
adenylosuccinate lyase (purB,adsL) 抗体
adenylosuccinate lyase (Mrub_2293) 抗体
adenylosuccinate lyase (MMAH_RS02975) 抗体
adenylosuccinate lyase (Arnit_0089) 抗体
adenylosuccinate lyase (Mesil_1058) 抗体
adenylosuccinate lyase (Slip_0597) 抗体
adenylosuccinate lyase (Trad_2452) 抗体
adenylosuccinate lyase (Deba_0652) 抗体
adenylosuccinate lyase (Toce_1174) 抗体
Adenylosuccinate lyase (Acear_2324) 抗体
Adenylosuccinate lyase (Igag_0272) 抗体
adenylosuccinate lyase (Saut_2156) 抗体
Adenylosuccinate lyase (Fbal_1996) 抗体
adenylosuccinate lyase (Ndas_2434) 抗体
adenylosuccinate lyase (Ilyop_0196) 抗体
adenylosuccinate lyase (Lbys_2961) 抗体
adenylosuccinate lyase (MFER_RS02920) 抗体
adenylosuccinate lyase (Palpr_2192) 抗体
adenylosuccinate lyase (Calni_0061) 抗体
adenylosuccinate lyase (Ftrac_3746) 抗体
L-Aspartase-like family protein (AT1G36280) 抗体
Adenylosuccinate lyase (Olsu_1764) 抗体
adenylosuccinate lyase (Adsl) 抗体
Adl 抗体
adsL 抗体
AMPS 抗体
ASASE 抗体
ASL 抗体
Asl 抗体
F15C21.8 抗体
F15C21_8 抗体
fi60b04 抗体
MGC53383 抗体
MGC69239 抗体
purB 抗体
wu:fi60b04 抗体
zgc:56061 抗体
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