This gene encodes a member of the ADAMTS (a disintegrin and metalloproteinase with thrombospondin motifs) and ADAMTS-like protein family. Members of the family share several distinct protein modules, including a propeptide region, a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. Individual members of this family differ in the number of C-terminal TS motifs, and some have unique C-terminal domains. The protein encoded by this gene lacks the protease domain, and is therefore of a member of the the ADAMTS-like protein subfamily. It is a secreted glycoprotein that binds the cell surface and extracellular matrix\; it also interacts with latent transforming growth factor beta binding protein 1. Mutations in this gene have been associated with geleophysic dysplasia. [provided by RefSeq, Feb 2009].
Piccolo, Sabatino, Mithbaokar, Polishchuck, Law, Magraner-Pardo, Pons, Polishchuck, Brunetti-Pierri: "Geleophysic dysplasia: novel missense variants and insights into ADAMTSL2 intracellular trafficking." in: Molecular genetics and metabolism reports, Vol. 21, pp. 100504, (2019) (PubMed).
Aviram, Zaffryar-Eilot, Hubmacher, Grunwald, Mäki, Myllyharju, Apte, Hasson: "Interactions between lysyl oxidases and ADAMTS proteins suggest a novel crosstalk between two extracellular matrix families." in: Matrix biology : journal of the International Society for Matrix Biology, Vol. 75-76, pp. 114-125, (2019) (PubMed).