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ADAMTS13 抗体

(ADAM Metallopeptidase with Thrombospondin Type 1 Motif, 13 (ADAMTS13))
This gene encodes a member of the ADAMTS (a disintegrin and metalloproteinase with thrombospondin motif) protein family. Members of the family share several distinct protein modules, including a propeptide region, a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. Individual members of this family differ in the number of C-terminal TS motifs, and some have unique C-terminal domains. The enzyme encoded by this gene is the von Willebrand Factor (vWF)-cleaving protease, which is responsible for cleaving at the site of Tyr842-Met843 of the vWF molecule. A deficiency of this enzyme is associated with thrombotic thrombocytopenic purpura. Alternative splicing of this gene generates multiple transcript variants encoding different isoforms. [provided by RefSeq, Nov 2008].

Active filters:

  • 抗原: ADAMTS13
  • Primary
Catalog no. 产品 适用 宿主 / 克隆类型 应用 价格和交货时间
ABIN7802416
ADAMTS13 抗体 ADAMTS13 · Primary Antibody 人 小鼠 Monoclonal 克隆位点 3H9
  • 100 μg
发货至: 中国
ABIN7802417
ADAMTS13 抗体 ADAMTS13 · Primary Antibody 人 小鼠 Monoclonal 克隆位点 17C7
  • 100 μg
发货至: 中国
ABIN7811211
ADAMTS13 抗体 ADAMTS13 · Primary Antibody 小鼠 兔 Polyclonal
  • 100 μg
发货至: 中国
ABIN6107943
ADAMTS13 抗体 (AA 738-905) (FITC) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • ELISA (ELISA: 所列应用)
  • 100 μL
  • 20 μL
  • 50 μL
发货至: 中国
ABIN6905977
ADAMTS13 抗体 (Alexa Fluor 680) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN6889914
ADAMTS13 抗体 (Alexa Fluor 555) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN6916528
ADAMTS13 抗体 (Alexa Fluor 647) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN7791262
Recombinant ADAMTS13 抗体 (Alexa Fluor 350) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791263
Recombinant ADAMTS13 抗体 (Alexa Fluor 405) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791264
Recombinant ADAMTS13 抗体 (Alexa Fluor 488) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791265
Recombinant ADAMTS13 抗体 (Alexa Fluor 555) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791266
Recombinant ADAMTS13 抗体 (Alexa Fluor 594) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791267
Recombinant ADAMTS13 抗体 (Alexa Fluor 647) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791268
Recombinant ADAMTS13 抗体 (Alexa Fluor 680) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791269
Recombinant ADAMTS13 抗体 (Alexa Fluor 750) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN7791270
Recombinant ADAMTS13 抗体 (Biotin) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
  • 100 μL
发货至: 中国
ABIN6857787
ADAMTS13 抗体 (Alexa Fluor 750) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN6817535
ADAMTS13 抗体 (Alexa Fluor 488) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN6833598
ADAMTS13 抗体 (Alexa Fluor 594) ADAMTS13 · Primary Antibody 人 兔 Polyclonal
  • 100 μL
发货至: 中国
ABIN6857788
Recombinant ADAMTS13 抗体 (Alexa Fluor 750) ADAMTS13 · Primary Antibody 人 兔 Monoclonal
  • 100 μL
发货至: 中国
Primary Antibody
适用
人
宿主
小鼠
克隆形成能力
Monoclonal
克隆
3H9
标记
unconjugated
抗体亚型
IgG2a, lambda
产品编号 ABIN7802416
Primary Antibody
适用
人
宿主
小鼠
克隆形成能力
Monoclonal
克隆
17C7
标记
unconjugated
抗体亚型
IgG2a
产品编号 ABIN7802417
Primary Antibody
适用
小鼠
宿主
兔
克隆形成能力
Polyclonal
标记
unconjugated
抗体亚型
IgG
产品编号 ABIN7811211
Primary Antibody
  • ELISA (ELISA: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
FITC
抗体亚型
IgG
抗原表位
AA 738-905
产品编号 ABIN6107943
100 μL (More quantities available)
发货至: 中国
获取报价
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 680
产品编号 ABIN6905977
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 555
产品编号 ABIN6889914
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 647
产品编号 ABIN6916528
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 350
蛋白类型
Recombinant Antibody
产品编号 ABIN7791262
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 405
蛋白类型
Recombinant Antibody
产品编号 ABIN7791263
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 488
蛋白类型
Recombinant Antibody
产品编号 ABIN7791264
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 555
蛋白类型
Recombinant Antibody
产品编号 ABIN7791265
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 594
蛋白类型
Recombinant Antibody
产品编号 ABIN7791266
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 647
蛋白类型
Recombinant Antibody
产品编号 ABIN7791267
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 680
蛋白类型
Recombinant Antibody
产品编号 ABIN7791268
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 750
蛋白类型
Recombinant Antibody
产品编号 ABIN7791269
Primary Antibody
  • WB (Western Blotting: 所列应用)
  • FACS (Flow Cytometry: 所列应用)
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Biotin
蛋白类型
Recombinant Antibody
产品编号 ABIN7791270
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 750
产品编号 ABIN6857787
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 488
产品编号 ABIN6817535
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Alexa Fluor 594
产品编号 ABIN6833598
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Monoclonal
标记
Alexa Fluor 750
蛋白类型
Recombinant Antibody
产品编号 ABIN6857788

Latest Publications for our ADAMTS13 抗体

Feng, Eyler, Zhang, Maga, Nester, Kroll, Smith, Afshar-Kharghan: "Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome." in: Blood, Vol. 122, Issue 8, pp. 1487-93, (2013) (PubMed).

Feng, Liang, Cruz, Vu, Zhou, Pemmaraju, Dong, Kroll, Afshar-Kharghan: "The interaction between factor H and Von Willebrand factor." in: PLoS ONE, Vol. 8, Issue 8, pp. e73715, (2013) (PubMed).

Hershko, Simhadri, Blaisdell, Hunt, Newell, Tseng, Hershko, Choi, Sauna, Wu, Bram, Komar, Kimchi-Sarfaty: "Cyclosporin A impairs the secretion and activity of ADAMTS13 (a disintegrin and metalloprotease with thrombospondin type 1 repeat)." in: The Journal of biological chemistry, Vol. 287, Issue 53, pp. 44361-71, (2012) (PubMed).

Hunt, Geetha, Allen, Hershko, Fathke, Kong, Plum, Struble, Soejima, Friedman, Garfield, Balaji, Kimchi-Sarfaty: "Detection of a secreted metalloprotease within the nuclei of liver cells." in: Molecular bioSystems, Vol. 7, Issue 6, pp. 2012-8, (2011) (PubMed).

Ganburged, Suda, Saito, Yamazaki, Isokawa, Moriyama: "Dilated capillaries, disorganized collagen fibers and differential gene expression in periodontal ligaments of hypomorphic fibrillin-1 mice." in: Cell and tissue research, Vol. 341, Issue 3, pp. 381-95, (2010) (PubMed).

Turner, Nolasco, Ruggeri, Moake: "Endothelial cell ADAMTS-13 and VWF: production, release, and VWF string cleavage." in: Blood, Vol. 114, Issue 24, pp. 5102-11, (2009) (PubMed).

Sen, Tyagi, Patibandla, Dean, Tyagi, Roberts, Lominadze: "Fibrinogen-induced endothelin-1 production from endothelial cells." in: American journal of physiology. Cell physiology, Vol. 296, Issue 4, pp. C840-7, (2009) (PubMed).

Chung, Popova, Jorgensen, Dong, Chandhoke, Bailey, Popov: "Degradation of circulating von Willebrand factor and its regulator ADAMTS13 implicates secreted Bacillus anthracis metalloproteases in anthrax consumptive coagulopathy." in: The Journal of biological chemistry, Vol. 283, Issue 15, pp. 9531-42, (2008) (PubMed).

Tao, Wang, Choi, Bernardo, Nishio, Sadler, López, Dong: "Cleavage of ultralarge multimers of von Willebrand factor by C-terminal-truncated mutants of ADAMTS-13 under flow." in: Blood, Vol. 106, Issue 1, pp. 141-3, (2005) (PubMed).

Dong: "Cleavage of ultra-large von Willebrand factor by ADAMTS-13 under flow conditions." in: Journal of thrombosis and haemostasis : JTH, Vol. 3, Issue 8, pp. 1710-6, (2005) (PubMed).

Aliases for ADAMTS13 抗体

ADAM metallopeptidase with thrombospondin type 1 motif 13 (ADAMTS13) 抗体
a disintegrin-like and metallopeptidase (reprolysin type) with thrombospondin type 1 motif, 13 (Adamts13) 抗体
ADAM metallopeptidase with thrombospondin type 1 motif, 13 (adamts13) 抗体
ADAM metallopeptidase with thrombospondin type 1 motif, 13 (Adamts13) 抗体
ADAM metallopeptidase with thrombospondin type 1 motif 13 (Adamts13) 抗体
ADAM-TS13 抗体
ADAMTS-13 抗体
ADAMTS13 抗体
C9orf8 抗体
Gm710 抗体
vWF-CP 抗体
VWFCP 抗体
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