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LEPRE1 抗体

(Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1))
This gene encodes an enzyme that is a member of the collagen prolyl hydroxylase family. These enzymes are localized to the endoplasmic reticulum and their activity is required for proper collagen synthesis and assembly. Mutations in this gene are associated with osteogenesis imperfecta type VIII. Three alternatively spliced transcript variants encoding different isoforms have been described. Other variants may exist, but their biological validity has not been determined. [provided by RefSeq, Aug 2011].
LEPRE1 抗体  (AA 1-100) LEPRE1 抗体  (AA 1-100) LEPRE1 抗体 (AA 1-100) (ABIN566242)

LEPRE1 适用: 人 WB, ELISA, IF, IHC (p) 宿主: 小鼠 Monoclonal 3C7 unconjugated

LEPRE1 抗体  (AA 1-390) LEPRE1 抗体  (AA 1-390) LEPRE1 抗体 (AA 1-390) (ABIN528557)

LEPRE1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated

LEPRE1 抗体 LEPRE1 抗体 LEPRE1 抗体 (ABIN1499129)

LEPRE1 适用: 人 WB, IHC, FACS, IHC (p) 宿主: 小鼠 Monoclonal 1A1 unconjugated

LEPRE1 抗体 by 适用

Find LEPRE1 抗体 for a variety of species such as anti-Human LEPRE1, anti-Mouse LEPRE1. The species listed below are among those available. Click on a link to go to the corresponding products.

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LEPRE1 抗体 by 克隆形成能力

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Find LEPRE1 抗体 with a specific conjugate such as APC, Biotin, FITC. The conjugates listed below are among those available. Click on a link to go to the corresponding products.

Popular LEPRE1 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, ELISA, IF, IHC (p)
Validations
  • (4)
  • (6)
Cat. No. ABIN566242
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (9)
  • (2)
Cat. No. ABIN528557
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Application WB, IHC, FACS, IHC (p)
Validations
  • (3)
Cat. No. ABIN1499129
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, FACS, IF
Validations
  • (3)
Cat. No. ABIN1499128
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (1)
Cat. No. ABIN6243368
Quantity 400 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (1)
Cat. No. ABIN528558
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (1)
Cat. No. ABIN6143144
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse
Application WB
Validations
  • (2)
Cat. No. ABIN4904219
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
Cat. No. ABIN2582331
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Application WB
Validations
Cat. No. ABIN2582332
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
Cat. No. ABIN1909621
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
Cat. No. ABIN1909624
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
Cat. No. ABIN1909622
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
Cat. No. ABIN1909623
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
Cat. No. ABIN1909625
Quantity 200 μL
Datasheet Datasheet

Latest Publications for our LEPRE1 抗体

Huang, Mei, Lv, Li, Zhang, Pan, Tan, Guo, Luo, Chen, Liang, Wu: "Targeted exome sequencing identifies novel compound heterozygous mutations in P3H1 in a fetus with osteogenesis imperfecta type VIII." in: Clinica chimica acta; international journal of clinical chemistry, Vol. 464, pp. 170-175, (2016) (PubMed).

Ohe, Aung, Meng, Kabasawa, Suto, Tamazawa, Yang, Kato, Yamakawa: "Localization of collagen modifying enzymes on fibroblastic reticular cells and follicular dendritic cells in non-neoplastic and neoplastic lymphoid tissues." in: Leukemia & lymphoma, Vol. 57, Issue 7, pp. 1687-96, (2016) (PubMed).

Cabral, Perdivara, Weis, Terajima, Blissett, Chang, Perosky, Makareeva, Mertz, Leikin, Tomer, Kozloff, Eyre, Yamauchi, Marini: "Abnormal type I collagen post-translational modification and crosslinking in a cyclophilin B KO mouse model of recessive osteogenesis imperfecta." in: PLoS genetics, Vol. 10, Issue 6, pp. e1004465, (2014) (PubMed).

Takagi, Ishii, Barnes, Weis, Amano, Tanaka, Fukuzawa, Nishimura, Eyre, Marini, Hasegawa: "A novel mutation in LEPRE1 that eliminates only the KDEL ER- retrieval sequence causes non-lethal osteogenesis imperfecta." in: PLoS ONE, Vol. 7, Issue 5, pp. e36809, (2012) (PubMed).

Pyott, Schwarze, Christiansen, Pepin, Leistritz, Dineen, Harris, Burton, Angle, Kim, Sussman, Weis, Eyre, Russell, McCarthy, Steiner, Byers: "Mutations in PPIB (cyclophilin B) delay type I procollagen chain association and result in perinatal lethal to moderate osteogenesis imperfecta phenotypes." in: Human molecular genetics, Vol. 20, Issue 8, pp. 1595-609, (2011) (PubMed).

Amor, Rauch, Gruenwald, Weis, Eyre, Roughley, Glorieux, Morello: "Severe osteogenesis imperfecta caused by a small in-frame deletion in CRTAP." in: American journal of medical genetics. Part A, Vol. 155A, Issue 11, pp. 2865-70, (2011) (PubMed).

Lai, Song, Hakala, Weintraub, Shiio: "Proteomic dissection of the von Hippel-Lindau (VHL) interactome." in: Journal of proteome research, Vol. 10, Issue 11, pp. 5175-82, (2011) (PubMed).

Baldridge, Lennington, Weis, Homan, Jiang, Munivez, Keene, Hogue, Pyott, Byers, Krakow, Cohn, Eyre, Lee, Morello: "Generalized connective tissue disease in Crtap-/- mouse." in: PLoS ONE, Vol. 5, Issue 5, pp. e10560, (2010) (PubMed).

Willaert, Malfait, Symoens, Gevaert, Kayserili, Megarbane, Mortier, Leroy, Coucke, De Paepe: "Recessive osteogenesis imperfecta caused by LEPRE1 mutations: clinical documentation and identification of the splice form responsible for prolyl 3-hydroxylation." in: Journal of medical genetics, Vol. 46, Issue 4, pp. 233-41, (2009) (PubMed).

van Dijk, Nesbitt, Zwikstra, Nikkels, Piersma, Fratantoni, Jimenez, Huizer, Morsman, Cobben, van Roij, Elting, Verbeke, Wijnaendts, Shaw, Högler, McKeown, Sistermans, Dalton, Meijers-Heijboer, Pals: "PPIB mutations cause severe osteogenesis imperfecta." in: American journal of human genetics, Vol. 85, Issue 4, pp. 521-7, (2009) (PubMed).

Aliases for LEPRE1 抗体

prolyl 3-hydroxylase 1 (P3H1) 抗体
prolyl 3-hydroxylase 1 (P3h1) 抗体
prolyl 3-hydroxylase 1 L homeolog (p3h1.L) 抗体
prolyl 3-hydroxylase 1 (p3h1) 抗体
2410024C15Rik 抗体
GROS1 抗体
Gros1 抗体
LEPRE1 抗体
MGC84556 抗体
OI8 抗体
P3H1 抗体
sb:cb953 抗体
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