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PYGL 抗体

(phosphorylase, Glycogen, Liver (PYGL))
This gene encodes a homodimeric protein that catalyses the cleavage of alpha-1,4-glucosidic bonds to release glucose-1-phosphate from liver glycogen stores. This protein switches from inactive phosphorylase B to active phosphorylase A by phosphorylation of serine residue 15. Activity of this enzyme is further regulated by multiple allosteric effectors and hormonal controls. Humans have three glycogen phosphorylase genes that encode distinct isozymes that are primarily expressed in liver, brain and muscle, respectively. The liver isozyme serves the glycemic demands of the body in general while the brain and muscle isozymes supply just those tissues. In glycogen storage disease type VI, also known as Hers disease, mutations in liver glycogen phosphorylase inhibit the conversion of glycogen to glucose and results in moderate hypoglycemia, mild ketosis, growth retardation and hepatomegaly. Alternative splicing results in multiple transcript variants encoding different isoforms.[provided by RefSeq, Feb 2011].

87 results

PYGL 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7438019
 
PYGL 适用: 人 WB, IHC, IP, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6146525
 
PYGL 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7154210
 
PYGL 适用: 人, 大鼠, 小鼠 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7237619
 
PYGL 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN948366
 
PYGL 适用: 大鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1173786
 
PYGL 适用: 人, 小鼠 WB, IHC (p) 宿主: 兔 Polyclonal RB53470 unconjugated
产品编号 ABIN6243863
 
PYGL 适用: 人, 猴 IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1049280
 
PYGL 适用: 人, 犬 IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN213380
 
PYGL 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1860385
 
PYGL 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1860384
 
PYGL 适用: 人, 大鼠, 小鼠 WB, IHC, IF, IC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7306772
 
PYGL 适用: 大鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7644371
 
PYGL 适用: 大鼠 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal 9# unconjugated
产品编号 ABIN7427786
 
PYGL 适用: 人, 大鼠, 小鼠 IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7262605
 
PYGL 适用: 人 WB, IHC, ELISA, IHC (p) 宿主: 兔 Polyclonal FITC
产品编号 ABIN2577841
 
PYGL 适用: 人 WB, IHC, ELISA, IHC (p) 宿主: 兔 Polyclonal HRP
产品编号 ABIN2577840
 
PYGL 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1173783
 
PYGL 适用: 人 ELISA, IHC (p), IF (cc), IF (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN708341
 
PYGL 适用: 人 ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN708343
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • Immunoprecipitation (IP)
    • Immunocytochemistry (ICC)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunofluorescence (fixed cells) (IF/ICC)
    • Flow Cytometry (FACS)
    • Immunochromatography (IC)
  • 适用
    • Human
    • Rat
    • Mouse
    • Dog
    • Monkey
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 13#
    • 15#
    • 2#
    • 9#
    • RB53470
  • 抗原表位
    • AA 451-550
    • AA 73-267
    • AA 2-846
    • AA 370-538
    • AA 603-750
    • AA 341-509
    • AA 633-820
    • AA 1-847
    • AA 1-280
    • AA 313-804
    • AA 797-847
    • AA 809-843
    • C-Term
    • Internal Region
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG2a kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Signalway
    • Biomatik
    • Cloud-Clone
    • Abbexa
    • Boster Bio
    • CUSABIO
    • Cohesion Biosciences
    • USBio

Latest Publications for our PYGL 抗体

Nogales-Gadea, Mormeneo, García-Consuegra, Rubio, Orozco, Arenas, Martín, Lucia, Gómez-Foix, Martí, Andreu: "Expression of glycogen phosphorylase isoforms in cultured muscle from patients with McArdle's disease carrying the p.R771PfsX33 PYGM mutation." in: PLoS ONE, Vol. 5, Issue 10, (2010) (PubMed).

Aliases for PYGL 抗体

glycogen phosphorylase L (PYGL) 抗体
phosphorylase, glycogen, liver (pygl) 抗体
phosphorylase, glycogen, liver S homeolog (pygl.S) 抗体
liver glycogen phosphorylase (Pygl) 抗体
glycogen phosphorylase L (Pygl) 抗体
GSD6 抗体
zgc:66314 抗体
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