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Galactosidase, alpha (GLA) Peptide

GLA 适用: 人 宿主: 合成 BP, WB
产品编号 ABIN977443
发货至: 中国
  • 抗原 See all GLA products
    GLA (Galactosidase, alpha (GLA))
    宿主
    资源
    • 1
    合成
    应用范围
    Blocking Peptide (BP), Western Blotting (WB)
    产品特性
    This is a synthetic peptide designed for use in combination with anti-GLA antibody (Catalog #: ARP54296_P050). It may block above mentioned antibody from binding to its target protein in western blot and/or immunohistochecmistry under proper experimental settings. There is no guarantee for its use in other applications.
    纯化方法
    Purified
  • 应用备注
    Each Investigator should determine their own optimal working dilution for specific applications.
    限制
    仅限研究用
  • 状态
    Lyophilized
    溶解方式
    Add 100 μL of sterile PBS. Final peptide concentration is 1 mg/mL in PBS.
    浓度
    1 mg/mL
    缓冲液
    Final peptide concentration is 1 mg/mL in PBS.
    注意事项
    Avoid repeated freeze-thaw cycles.
    储存条件
    -20 °C
    储存方法
    For longer periods of storage, store at -20°C. Avoid repeat freeze-thaw cycles.
  • 抗原
    GLA (Galactosidase, alpha (GLA))
    别名
    GALA Peptide, Ags Peptide, zgc:101584 Peptide, MGC130872 Peptide, SMU.877 Peptide, SCF11.21 Peptide, AO090005000217 Peptide, alpha-GAL Peptide, galactosidase alpha Peptide, galactosidase, alpha Peptide, galactosidase alpha S homeolog Peptide, alpha-galactosidase Peptide, aga Peptide, alpha-galactosidase A Peptide, GLA Peptide, Gla Peptide, gla Peptide, gla.S Peptide, agaN Peptide, aga Peptide, agaL Peptide, SCO0541 Peptide, rafA Peptide, melA Peptide, galA Peptide, ANI_1_2528074 Peptide, ANI_1_1502124 Peptide, AOR_1_390174 Peptide, CpipJ_CPIJ002066 Peptide, MCYG_00962 Peptide, MCYG_00791 Peptide, Tsp_02909 Peptide, Tsp_02508 Peptide
    背景
    GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. Publication Note: This RefSeq record includes a subset of the publications that are available for this gene. Please see the Entrez Gene record to access additional publications.

    Alias Symbols: GALA

    Protein Interaction Partner: GLA,OTUD4

    Protein Size: 429
    分子量
    45 kDa
    基因ID
    2717
    NCBI登录号
    NM_000169, NP_000160
    UniProt
    P06280
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