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Propionyl CoA Carboxylase, alpha Polypeptide 抗体

(Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))
The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010].

34 results :

PCCA 适用: 人, 大鼠 WB, IHC (p) 宿主: 兔 Polyclonal RB31944 unconjugated
产品编号 ABIN656262
 
PCCA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
Pubmed 2 references
产品编号 ABIN518660
 
PCCA 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7164812
 
PCCA 适用: 人, 小鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6264065
 
PCCA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5014164
 
PCCA 适用: 人, 小鼠, 大鼠, Cow, 马, 斑马鱼, 犬, Pig, 兔 WB, IHC 宿主: 兔 Polyclonal unconjugated
Pubmed 1 reference
产品编号 ABIN2777736
 
PCCA 适用: 人, 小鼠, Cow, 马, 斑马鱼, 兔 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6737708
 
PCCA 适用: 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7264805
 
PCCA 适用: 人, 小鼠, 大鼠, Cow, 马, 斑马鱼, 犬, Pig, 小鸡 WB, IHC, IHC (p), IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2626600
 
PCCA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6145279
 
PCCA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN631082
 
PCCA 适用: 人 WB, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN954025
 
PCCA 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7164815
 
PCCA 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7164814
 
PCCA 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7164813
 
PCCA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7644909
 
PCCA 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7117843
 
PCCA 适用: 人, 小鼠 WB, IHC (fp) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7454579
 
PCCA 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7570899
 
PCCA 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7469540
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • ELISA
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunoprecipitation (IP)
    • Enzyme Immunoassay (EIA)
    • Flow Cytometry (FACS)
    • Immunofluorescence (IF)
    • Immunohistochemistry (Formalin-fixed Paraffin-embedded Sections) (IHC (fp))
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Horse
    • Zebrafish (Danio rerio)
    • Dog
    • Pig
    • Rabbit
    • Chicken
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
  • 克隆
    • RB31944
  • 抗原表位
    • AA 362-390
    • AA 585-720
    • AA 580-728
    • AA 1-703
    • AA 336-365
    • AA 678-728
    • C-Term
    • N-Term
    • AA 38-87
    • AA 403-728
    • AA 449-728
    • Center
    • Internal Region
    • Middle Region
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • APC
    • PE
  • 抗体亚型
    • IgG
    • Ig Fraction
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Abbexa
    • Biomatik
    • USBio
    • Abcepta
    • Acris
    • Aviva Systems Biology
    • Boster Bio
    • Cloud-Clone
    • St John's Laboratory

Latest Publications for our Propionyl CoA Carboxylase, alpha Polypeptide 抗体

Majtan, Kraus: "Folding and activity of mutant cystathionine ?-synthase depends on the position and nature of the purification tag: characterization of the R266K CBS mutant." in: Protein expression and purification, Vol. 82, Issue 2, pp. 317-24, (2012) (PubMed).

Rincón, Aguado, Desviat, Sánchez-Alcudia, Ugarte, Pérez: "Propionic and methylmalonic acidemia: antisense therapeutics for intronic variations causing aberrantly spliced messenger RNA." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1262-70, (2011) (PubMed).

Chandler, Chandrasekaran, Carrillo-Carrasco, Senac, Hofherr, Barry, Venditti: "Adeno-associated virus serotype 8 gene transfer rescues a neonatal lethal murine model of propionic acidemia." in: Human gene therapy, Vol. 22, Issue 4, pp. 477-81, (2011) (PubMed).

Aliases for Propionyl CoA Carboxylase, alpha Polypeptide 抗体

propionyl-CoA carboxylase alpha subunit (PCCA) 抗体
propionyl-CoA carboxylase alpha subunit (Pcca) 抗体
propionyl-COA carboxylase alpha chain, mitochondrial (BMEI0800) 抗体
propionyl-CoA carboxylase alpha chain (pccA) 抗体
propionyl-CoA carboxylase alpha chain (NRI_0781) 抗体
zinc finger CCCH-type containing 13 (zc3h13) 抗体
propionyl-Coenzyme A carboxylase, alpha polypeptide (Pcca) 抗体
propionyl CoA carboxylase, alpha polypeptide (pcca) 抗体
propionyl-CoA carboxylase alpha subunit L homeolog (pcca.L) 抗体
C79630 抗体
pcca 抗体
wu:fb92g02 抗体
zgc:66359 抗体
zgc:100925 抗体
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