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PANK2 抗体

(Pantothenate Kinase 2 (PANK2))
This gene encodes a protein belonging to the pantothenate kinase family and is the only member of that family to be expressed in mitochondria. Pantothenate kinase is a key regulatory enzyme in the biosynthesis of coenzyme A (CoA) in bacteria and mammalian cells. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by acyl CoA species. Mutations in this gene are associated with HARP syndrome and pantothenate kinase-associated neurodegeneration (PKAN), formerly Hallervorden-Spatz syndrome. Alternative splicing, involving the use of alternate first exons, results in multiple transcripts encoding different isoforms. [provided by RefSeq, Jul 2008].

51 results

PANK2 适用: 人, 大鼠, 犬, 猴 WB, IHC, IF, IHC (p), FACS 宿主: 小鼠 Monoclonal 3H9 unconjugated
产品编号 ABIN1500026
 
PANK2 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7162603
 
PANK2 适用: 人 WB, ELISA, IHC (p) 宿主: 小鼠 Monoclonal 2B12 unconjugated
产品编号 ABIN566414
 
PANK2 适用: 人 WB, ELISA, IF, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6264029
 
PANK2 适用: 人, 大鼠, 犬, Cow, 马, 绵羊, Pig, Bat WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6748470
 
PANK2 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7269169
 
PANK2 适用: 人 WB, IF, FACS 宿主: 小鼠 Monoclonal 3G4 unconjugated
产品编号 ABIN2728204
 
PANK2 适用: 小鼠 WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1386810
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN5008315
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN5008316
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2805063
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN1398504
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN1398503
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5.5
产品编号 ABIN1416373
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy7
产品编号 ABIN1416374
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5
产品编号 ABIN1416372
 
PANK2 适用: 小鼠 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal HRP
产品编号 ABIN1416376
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy3
产品编号 ABIN1416371
 
PANK2 适用: 小鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal FITC
产品编号 ABIN1398506
 
PANK2 适用: 小鼠 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1398505
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunofluorescence (IF)
    • Immunohistochemistry (IHC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Flow Cytometry (FACS)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunocytochemistry (ICC)
    • Immunoprecipitation (IP)
    • Immunofluorescence (fixed cells) (IF/ICC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Horse
    • Pig
    • Bat
    • Guinea Pig
    • Monkey
    • Rabbit
    • Sheep
    • Zebrafish (Danio rerio)
    • Hamster
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 3H9
    • 2B12
    • 3G4
    • 4B3
    • RB5486
    • RB5487
  • 抗原表位
    • AA 401-500
    • AA 180-210
    • AA 437-490
    • AA 65-95
    • N-Term
    • AA 113-162
    • AA 205-260
    • AA 300-400
    • AA 308-357
    • AA 351-400
    • AA 459-508
    • C-Term
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • APC
    • PE
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • IgG2a
    • Ig Fraction
    • IgG1
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Abbexa
    • Abcepta
    • Aviva Systems Biology
    • Biomatik
    • OriGene

Latest Publications for our PANK2 抗体

Santambrogio, Dusi, Guaraldo, Rotundo, Broccoli, Garavaglia, Tiranti, Levi: "Mitochondrial iron and energetic dysfunction distinguish fibroblasts and induced neurons from pantothenate kinase-associated neurodegeneration patients." in: Neurobiology of disease, (2015) (PubMed).

Huang, Chu, Jiang, Chen, Zhang, Zeng: "Glycyrrhizin suppresses lung adenocarcinoma cell growth through inhibition of thromboxane synthase." in: Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology, Vol. 33, Issue 2, pp. 375-88, (2014) (PubMed).

Zeman, Lin, Freire, Cimprich: "DNA damage-specific deubiquitination regulates Rad18 functions to suppress mutagenesis." in: The Journal of cell biology, Vol. 206, Issue 2, pp. 183-97, (2014) (PubMed).

Barrett, Fang, Gargano, Markovich, Kocarek, Runge-Morris: "Regulation of murine hepatic hydroxysteroid sulfotransferase expression in hyposulfatemic mice and in a cell model of 3'-phosphoadenosine-5'-phosphosulfate deficiency." in: Drug metabolism and disposition: the biological fate of chemicals, Vol. 41, Issue 8, pp. 1505-13, (2013) (PubMed).

Brunetti, Dusi, Morbin, Uggetti, Moda, DAmato, Giordano, dAmati, Cozzi, Levi, Hayflick, Tiranti: "Pantothenate kinase-associated neurodegeneration: altered mitochondria membrane potential and defective respiration in Pank2 knock-out mouse model." in: Human molecular genetics, Vol. 21, Issue 24, pp. 5294-305, (2012) (PubMed).

Hörtnagel, Prokisch, Meitinger: "An isoform of hPANK2, deficient in pantothenate kinase-associated neurodegeneration, localizes to mitochondria." in: Human molecular genetics, Vol. 12, Issue 3, pp. 321-7, (2003) (PubMed).

Houlden, Lincoln, Farrer, Cleland, Hardy, Orrell: "Compound heterozygous PANK2 mutations confirm HARP and Hallervorden-Spatz syndromes are allelic." in: Neurology, Vol. 61, Issue 10, pp. 1423-6, (2003) (PubMed).

Ching, Westaway, Gitschier, Higgins, Hayflick: "HARP syndrome is allelic with pantothenate kinase-associated neurodegeneration." in: Neurology, Vol. 58, Issue 11, pp. 1673-4, (2002) (PubMed).

Aliases for PANK2 抗体

pantothenate kinase 2 (PANK2) 抗体
pantothenate kinase 2 (Tsp_01576) 抗体
pantothenate kinase 2, mitochondrial (LOC100539295) 抗体
pantothenate kinase 2 (Pank2) 抗体
ribonuclease A family member 11 (inactive) (RNASE11) 抗体
4933409I19Rik 抗体
AI642621 抗体
ATPANK2 抗体
C20orf48 抗体
F10M6.180 抗体
F10M6_180 抗体
HARP 抗体
HSS 抗体
NBIA1 抗体
PANK2 抗体
pantothenate kinase 2 抗体
PKAN 抗体
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