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OPA3 抗体

(Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3))
The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2009].

40 results :

OPA3 适用: 人 IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7162247
 
OPA3 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7162248
 
OPA3 适用: 人, 小鼠, 大鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7264051
 
OPA3 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
Pubmed 1 reference
产品编号 ABIN529218
 
OPA3 适用: 人 WB, IHC, ICC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6263824
 
OPA3 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5014057
 
OPA3 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5014056
 
OPA3 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5014055
 
OPA3 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1B8 unconjugated
产品编号 ABIN949672
 
OPA3 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6746679
 
OPA3 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN929355
 
OPA3 适用: 小鼠 IF (cc), IF (p), ICC, IHC (fro), IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6989915
 
OPA3 适用: 小鼠 IHC (fro), IHC (p) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN6982790
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN6978720
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN6980374
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN6976998
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN6981286
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN6979515
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN6977859
 
OPA3 适用: 小鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN6982258
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunocytochemistry (ICC)
    • Immunoprecipitation (IP)
    • ELISA
    • Immunofluorescence (IF)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Flow Cytometry (FACS)
  • 适用
    • Mouse
    • Human
    • Rat
    • Pig
  • 论文引用
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 1B8
  • 抗原表位
    • AA 1-100
    • AA 25-179
    • AA 1-179
    • AA 1-200
    • AA 11-179
    • AA 23-179
    • C-Term
    • AA 103-179
    • AA 103-180
    • AA 95-144
    • Internal Region
  • 标记
    • 非结合性
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Biotin
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
    • FITC
    • HRP
  • 抗体亚型
    • IgG
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Biomatik
    • Cloud-Clone
    • USBio
    • Abbexa
    • Aviva Systems Biology
    • Boster Bio
    • Wuhan Fine biotech

Latest Publications for our OPA3 抗体

Powell, Davies, Taylor, Wride, Votruba: "Mitochondrial localization and ocular expression of mutant Opa3 in a mouse model of 3-methylglutaconicaciduria type III." in: Investigative ophthalmology & visual science, Vol. 52, Issue 7, pp. 4369-80, (2011) (PubMed).

Aliases for OPA3 抗体

optic atrophy 3 (opa3) 抗体
optic atrophy 3 (Opa3) 抗体
OPA3, outer mitochondrial membrane lipid metabolism regulator (OPA3) 抗体
OPA3, outer mitochondrial membrane lipid metabolism regulator (Opa3) 抗体
D630048P19Rik 抗体
Gm472 抗体
Gm1425 抗体
MGA3 抗体
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