LONP1 抗体
(Lon Peptidase 1, Mitochondrial (LONP1))
This gene encodes a mitochondrial matrix protein that belongs to the Lon family of ATP-dependent proteases. This protein mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides in the mitochondrial matrix. It may also have a chaperone function in the assembly of inner membrane protein complexes, and participate in the regulation of mitochondrial gene expression and maintenance of the integrity of the mitochondrial genome. Decreased expression of this gene has been noted in a patient with hereditary spastic paraplegia (PMID:18378094). Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Feb 2013].
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Latest Publications for our LONP1 抗体
: "Concentration of mitochondrial DNA mutations by cytoplasmic transfer from platelets to cultured mouse cells." in: PLoS ONE, Vol. 14, Issue 3, pp. e0213283, (2019) (PubMed).: "Reciprocal Roles of Tom7 and OMA1 during Mitochondrial Import and Activation of PINK1." in: Molecular cell, Vol. 73, Issue 5, pp. 1028-1043.e5, (2019) (PubMed).
: "Loss of the Drosophila m-AAA mitochondrial protease paraplegin results in mitochondrial dysfunction, shortened lifespan, and neuronal and muscular degeneration." in: Cell death & disease, Vol. 9, Issue 3, pp. 304, (2018) (PubMed).
: "Defects in the mitochondrial-tRNA modification enzymes MTO1 and GTPBP3 promote different metabolic reprogramming through a HIF-PPARγ-UCP2-AMPK axis." in: Scientific reports, Vol. 8, Issue 1, pp. 1163, (2018) (PubMed).
: "Lon protease inactivation in Drosophila causes unfolded protein stress and inhibition of mitochondrial translation." in: Cell death discovery, Vol. 4, pp. 51, (2018) (PubMed).
: "PINK1-Parkin pathway activity is regulated by degradation of PINK1 in the mitochondrial matrix." in: PLoS genetics, Vol. 10, Issue 5, pp. e1004279, (2014) (PubMed).
: "The accumulation of misfolded proteins in the mitochondrial matrix is sensed by PINK1 to induce PARK2/Parkin-mediated mitophagy of polarized mitochondria." in: Autophagy, Vol. 9, Issue 11, pp. 1750-7, (2013) (PubMed).
: "Splenomegaly as a primary manifestation of Gaucher disease in a young adult woman." in: Case reports in gastroenterology, Vol. 2, Issue 3, pp. 474-8, (2011) (PubMed).
: "Proteomics analysis reveals novel components in the detergent-insoluble subproteome in Alzheimer's disease." in: Journal of proteome research, Vol. 8, Issue 11, pp. 5069-79, (2009) (PubMed).
: "Thermodynamic characterization of specific interactions between the human Lon protease and G-quartet DNA." in: Nucleic acids research, Vol. 36, Issue 4, pp. 1273-87, (2008) (PubMed).
Aliases for LONP1 抗体
lon peptidase 1, mitochondrial (LONP1) 抗体lon peptidase 1, mitochondrial (lonp1) 抗体
lon peptidase 1, mitochondrial (Lonp1) 抗体
ATP-dependent Lon protease (PIM1) 抗体
1200017E13Rik 抗体
fc64d11 抗体
hLON 抗体
LON 抗体
Lon 抗体
LonHS 抗体
LONP 抗体
PIM1 抗体
PRSS15 抗体
prss15 抗体
Prss15 抗体
wu:fc64d11 抗体
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