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L2HGDH 产品

(L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation. [provided by RefSeq, Jul 2008].

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Featured L2HGDH Categories

L2HGDH 抗体

High quality antibodies with extensive validation data.

L2HGDH ELISA试剂盒

Reliable ELISA kits for a wide range of species.

L2HGDH 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended L2HGDH 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human, Mouse
Application WB, IHC
Validations
  • (3)
Cat. No. ABIN7264049
Quantity 200 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IHC
Validations
  • (3)
Cat. No. ABIN6262899
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, WB, IHC
Validations
  • (2)
Cat. No. ABIN7157773
Quantity 100 μL
Datasheet Datasheet

Recommended L2HGDH ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method
Validations
Cat. No. ABIN1139877
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method
Validations
Cat. No. ABIN1139878
Quantity 96 tests
Datasheet Datasheet
Reactivity Cow
Analytical Method
Validations
Cat. No. ABIN1139876
Quantity 96 tests
Datasheet Datasheet

Recommended L2HGDH 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN7123703
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN7123702
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1309094
Quantity 25 μg
Datasheet Datasheet

Synonyms and alternative names related to L2HGDH

L-2-hydroxyglutarate dehydrogenase (L2hgdh), L-2-hydroxyglutarate dehydrogenase (L2HGDH), BC016226, C14orf160, RGD1306250

Protein level used designations for L2HGDH

  • L-2-hydroxyglutarate dehydrogenase, mitochondrial
  • 2-hydroxyglutarate dehydrogenase
  • L-alpha-hydroxyglutarate dehydrogenase
  • alpha-hydroxyglutarate oxidoreductase
  • alpha-ketoglutarate reductase
  • duranin
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