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IDUA 抗体

(Iduronidase, alpha-L- (IDUA))
This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008].

39 results

IDUA 适用: 人 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB26860 unconjugated
产品编号 ABIN651536
 
IDUA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7441517
 
IDUA 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7143895
 
IDUA 适用: 人, 小鼠 ELISA, WB 宿主: 兔 Polyclonal unconjugated
Pubmed 1 reference
产品编号 ABIN6389869
 
IDUA 适用: 人, 小鼠 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7245281
 
IDUA 适用: 大鼠 ELISA, WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1713845
 
IDUA 适用: 人, 小鼠, 豚鼠, 马, Cow, Hamster WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2622290
 
IDUA 适用: 人 ELISA, WB 宿主: 小鼠 Monoclonal 452619 unconjugated
Pubmed 2 references
产品编号 ABIN603316
 
IDUA 适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal unconjugated
产品编号 ABIN7640478
 
IDUA 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7143898
 
IDUA 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7143897
 
IDUA 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7143896
 
IDUA 适用: 人 ELISA, WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7569718
 
IDUA 适用: 人 ELISA, WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7134176
 
IDUA 适用: 人, 小鼠, 大鼠, 豚鼠, 马, 猴 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6751893
 
IDUA 适用: 人 ELISA, WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2607561
 
IDUA 适用: 人 ELISA, WB, IHC, FACS 宿主: 兔 Polyclonal PE
产品编号 ABIN1904399
 
IDUA 适用: 人 ELISA, WB, IHC, FACS 宿主: 兔 Polyclonal FITC
产品编号 ABIN1904398
 
IDUA 适用: 人 ELISA, WB, IHC, FACS 宿主: 兔 Polyclonal APC
产品编号 ABIN1904396
 
IDUA 适用: 人 ELISA, WB, IHC, FACS 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1904397
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Flow Cytometry (FACS)
    • Immunoprecipitation (IP)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Immunofluorescence (fixed cells) (IF/ICC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Guinea Pig
    • Horse
    • Cow
    • Dog
    • Hamster
    • Monkey
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
    • Sheep
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 452619
    • RB26860
  • 抗原表位
    • AA 236-264
    • AA 28-653
    • AA 26-653
    • AA 28-306
    • AA 1-87
    • AA 101-200
    • AA 121-170
    • AA 509-558
    • C-Term
    • Center
    • Middle Region
    • N-Term
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • APC
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • PE
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Signalway
    • Aviva Systems Biology
    • Biomatik
    • Abbexa
    • Abcepta
    • Boster Bio
    • CUSABIO
    • RayBiotech

Latest Publications for our IDUA 抗体

Adachi, Pan, He, Chen, Klein, Platenburg, Morais, Boutz, Yu: "Targeted pseudouridylation: An approach for suppressing nonsense mutations in disease genes." in: Molecular cell, Vol. 83, Issue 4, pp. 637-651.e9, (2023) (PubMed).

Gutierrez-Valdes, Häkkinen, Lemasson, de Groot, Ele-Ekouna, Guillet, Cardon, Ritala: "Improving yield of a recombinant biologic in a Brassica hairy root manufacturing process." in: Biotechnology and bioengineering, (2022) (PubMed).

Cardon, Pallisse, Bardor, Caron, Vanier, Ele Ekouna, Lerouge, Boitel-Conti, Guillet: "Brassica rapa hairy root based expression system leads to the production of highly homogenous and reproducible profiles of recombinant human alpha-L-iduronidase." in: Plant biotechnology journal, Vol. 17, Issue 2, pp. 505-516, (2019) (PubMed).

Aliases for IDUA 抗体

iduronidase, alpha-L- (IDUA) 抗体
iduronidase, alpha-L- (Idua) 抗体
iduronidase, alpha-L- L homeolog (idua.L) 抗体
iduronidase, alpha-L- (idua) 抗体
alpha-L-iduronidase (LOC5564727) 抗体
6030426D08 抗体
alpha-L-iduronidase 抗体
IDA 抗体
IDUA 抗体
MGC80842 抗体
MPS1 抗体
si:ch211-12e13.9 抗体
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