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IDS 抗体

(Iduronate 2-Sulfatase (IDS))
Iduronate-2-sulfatase is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations in this X-chromosome gene that result in enzymatic deficiency lead to the sex-linked Mucopolysaccharidosis Type II, also known as Hunter Syndrome. Iduronate-2-sulfatase has a strong sequence similarity with human arylsulfatases A, B, and C, and human glucosamine-6-sulfatase. Multiple alternatively spliced transcript variants that encode different protein isoforms have been described. [provided by RefSeq, Oct 2009].

51 results

IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2814634
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN2176099
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN2176097
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN2176098
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN2176096
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal FITC
产品编号 ABIN2176105
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy7
产品编号 ABIN2176104
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5.5
产品编号 ABIN2176103
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5
产品编号 ABIN2176102
 
IDS 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy3
产品编号 ABIN2176101
 
IDS 适用: 人 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN2176100
 
IDS 适用: 人 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal HRP
产品编号 ABIN2176106
 
IDS 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7640475
 
IDS 适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal unconjugated
产品编号 ABIN7640477
 
IDS 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7640476
 
IDS 适用: 人 WB, IHC, ELISA, IF 宿主: 小鼠 Monoclonal 2D2 unconjugated
产品编号 ABIN7115175
 
IDS 适用: 人 WB, ELISA, FACS 宿主: 小鼠 Monoclonal AT6H4 unconjugated
产品编号 ABIN7596018
 
IDS 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7569717
 
IDS 适用: 人 WB, IF, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7509869
 
IDS 适用: 人, 猴 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2622289
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • ELISA
    • Immunoprecipitation (IP)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Flow Cytometry (FACS)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunofluorescence (fixed cells) (IF/ICC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Dog
    • Monkey
    • Cow
    • Guinea Pig
    • Rabbit
  • 图像
  • 仅无防腐剂
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
    • Goat
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 1D9
    • 3B4
    • 2D2
    • 4G2
    • AT6H4
  • 抗原表位
    • AA 101-200
    • AA 1-550
    • AA 26-550
    • AA 95-289
    • AA 1-312
    • AA 107-363
    • AA 180-448
    • AA 430-448
    • N-Term
    • AA 154-203
    • AA 34-290
    • AA 38-137
    • C-Term
    • Internal Region
  • 标记
    • 非结合性
    • Biotin
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
    • FITC
    • HRP
  • 抗体亚型
    • IgG
    • IgG2a
    • IgM kappa
    • IgG1
    • IgG2b kappa
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Verified
  • Supplier
    • antibodies-online
    • Biomatik
    • Cloud-Clone
    • Abbexa
    • Aviva Systems Biology
    • Boster Bio

Latest Publications for our IDS 抗体

Bellesso, Salvalaio, Lualdi, Tognon, Costa, Braghetta, Giraudo, Stramare, Rigon, Filocamo, Tomanin, Moro: "FGF signaling deregulation is associated with early developmental skeletal defects in animal models for mucopolysaccharidosis type II (MPSII)." in: Human molecular genetics, Vol. 27, Issue 13, pp. 2262-2275, (2019) (PubMed).

Keeratichamroen, Cairns, Wattanasirichaigoon, Wasant, Ngiwsara, Suwannarat, Pangkanon, Kuptanon, Tanpaiboon, Rujirawat, Liammongkolkul, Svasti: "Molecular analysis of the iduronate-2-sulfatase gene in Thai patients with Hunter syndrome." in: Journal of inherited metabolic disease, Vol. 31 Suppl 2, pp. S303-11, (2011) (PubMed).

Aliases for IDS 抗体

iduronate 2-sulfatase (IDS) 抗体
iduronate 2-sulfatase (CpipJ_CPIJ004938) 抗体
iduronate 2-sulfatase (ids) 抗体
iduronate 2-sulfatase (Ids) 抗体
AW214631 抗体
mps2 抗体
MPS2 抗体
sids 抗体
SIDS 抗体
zgc:158245 抗体
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