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HPS4 产品

(Hermansky-Pudlak Syndrome 4 (HPS4))
This gene encodes a protein component of biogenesis of lysosome-related organelles complexes (BLOC). BLOC complexes are important for the formation of endosomal-lysosomal organelles such as melanosomes and platelet dense granules. Mutations in this gene result in subtype 4 of Hermansky-Pudlak syndrome, a form of albinism. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2012].

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Featured HPS4 Categories

HPS4 抗体

High quality antibodies with extensive validation data.

HPS4 ELISA试剂盒

Reliable ELISA kits for a wide range of species.

HPS4 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended HPS4 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (7)
Cat. No. ABIN7443911
Quantity 100 μL
Datasheet Datasheet
Reactivity Mouse
Application WB, IHC, IP, ICC
Validations
  • (5)
Cat. No. ABIN7443896
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IF
Validations
  • (3)
Cat. No. ABIN7258952
Quantity 200 μL
Datasheet Datasheet

Recommended HPS4 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1743199
Quantity 96 tests
Datasheet Datasheet
Reactivity Sheep
Analytical Method
Validations
Cat. No. ABIN1774104
Quantity 96 tests
Datasheet Datasheet
Reactivity Dog
Analytical Method
Validations
Cat. No. ABIN1769208
Quantity 96 tests
Datasheet Datasheet

Recommended HPS4 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Tobacco (Nicotiana tabacum)
Validations
  • (1)
Cat. No. ABIN3081654
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Tobacco (Nicotiana tabacum)
Validations
  • (1)
Cat. No. ABIN3127932
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7417468
Quantity 100 μg
Datasheet Datasheet

Synonyms and alternative names related to HPS4

HPS4, biogenesis of lysosomal organelles complex 3 subunit 2 (HPS4), HPS4, biogenesis of lysosomal organelles complex 3 subunit 2 (Hps4), 2010205O06Rik, AU040608, BLOC-3, C130020P05Rik, LE, le, mKIAA1667

Protein level used designations for HPS4

  • Hermansky-Pudlak syndrome 4 protein
  • light-ear protein homolog
  • Hermansky-Pudlak syndrome 4 protein homolog
  • light ear
  • light-ear protein
  • Hermansky-Pudlak syndrome 4 homolog
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