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GNS 抗体
(Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. [provided by RefSeq, Jul 2008].
Recommended next Filters:
GNS
适用: 人
WB, IHC, ELISA
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
WB
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
IHC, ELISA
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
WB, IHC (p), FACS
宿主: 兔
Polyclonal
RB19341
unconjugated
GNS
适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, 斑马鱼
WB, IHC
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
WB, IHC, FACS
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
WB
宿主: 小鼠
Polyclonal
unconjugated
GNS
适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴
WB
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 斑马鱼, Bat, 猴
WB
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人, 小鼠, 大鼠
WB
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人, 小鼠, 大鼠
WB, ELISA
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
WB, IHC (p)
宿主: 兔
Polyclonal
RB19340
unconjugated
GNS
适用: 人
ELISA, IF (cc), IF (p), IHC (p), IHC (fro), ICC
宿主: 兔
Polyclonal
unconjugated
GNS
适用: 人
ELISA, IHC (p), IHC (fro)
宿主: 兔
Polyclonal
Biotin
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 750
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 680
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 555
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 488
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 350
GNS
适用: 人
IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 647
Target information, Synonyms, Latest references
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