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GBE1 抗体

(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008].

51 results :

GBE1 适用: 人 WB, IHC, IP, FACS, IHC (p) 宿主: 小鼠 Monoclonal 5B7 unconjugated
产品编号 ABIN1498396
 
GBE1 适用: 人 WB, IF, IP, FACS 宿主: 小鼠 Monoclonal 4D9 unconjugated
产品编号 ABIN1498395
 
GBE1 适用: 人 WB, IHC, IF, IP, FACS 宿主: 小鼠 Monoclonal 1D11 unconjugated
Pubmed 2 references
产品编号 ABIN2721750
 
GBE1 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7142066
 
GBE1 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN947904
 
GBE1 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
Pubmed 2 references
产品编号 ABIN561010
 
GBE1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN515961
 
GBE1 适用: 人, 小鼠 WB, IF 宿主: 兔 Polyclonal RB24029 unconjugated
产品编号 ABIN653459
 
GBE1 适用: 人, 小鼠 WB, IF, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN952469
 
GBE1 适用: 人 WB, ELISA, IF (cc), IF (p), ICC, IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1713806
 
GBE1 适用: 人 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1700304
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN5003256
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN5003255
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN1698491
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN1694852
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN1696680
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN1693037
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2813610
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy3
产品编号 ABIN1702117
 
GBE1 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy7
产品编号 ABIN1707697
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunofluorescence (IF)
    • Immunohistochemistry (IHC)
    • Immunocytochemistry (ICC)
    • Flow Cytometry (FACS)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunoprecipitation (IP)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Enzyme Immunoassay (EIA)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Guinea Pig
    • Horse
    • Rabbit
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 4D9
    • 5B7
    • 1D11
    • 3B4
    • RB24029
  • 抗原表位
    • AA 101-200
    • AA 527-556
    • AA 1-300
    • AA 1-702
    • AA 534-564
    • AA 176-225
    • AA 605-702
    • AA 79-515
    • Center
    • Internal Region
    • Middle Region
    • N-Term
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • APC
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
    • PE
  • 抗体亚型
    • IgG
    • IgG1
    • IgG2a
    • Ig Fraction
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Signalway
    • Abbexa
    • Abcepta
    • Acris
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • OriGene
    • USBio

Latest Publications for our GBE1 抗体

Colombo, Pagliarani, Testolin, Salsano, Napoli, Bordoni, Salani, DAdda, Morandi, Farina, Magri, Riva, Prelle, Sciacco, Comi, Moggio: "Adult polyglucosan body disease: clinical and histological heterogeneity of a large Italian family." in: Neuromuscular disorders : NMD, Vol. 25, Issue 5, pp. 423-8, (2015) (PubMed).

Irimia, Tagliabracci, Meyer, Segvich, DePaoli-Roach, Roach: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." in: The Journal of biological chemistry, (2015) (PubMed).

Orhan Akman, Emmanuele, Kurt, Kurt, Sheiko, DiMauro, Craigen: "A novel mouse model that recapitulates adult-onset glycogenosis type 4." in: Human molecular genetics, Vol. 24, Issue 23, pp. 6801-10, (2015) (PubMed).

Kakhlon, Glickstein, Feinstein, Liu, Baba, Terashima, Akman, Dimauro, Lossos: "Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase." in: Journal of neurochemistry, Vol. 127, Issue 1, pp. 101-13, (2013) (PubMed).

Akman, Sheiko, Tay, Finegold, Dimauro, Craigen: "Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV." in: Human molecular genetics, Vol. 20, Issue 22, pp. 4430-9, (2011) (PubMed).

Aliases for GBE1 抗体

1,4-alpha-glucan branching protein GlgB (glgB) 抗体
1,4-alpha-glucan branching protein (glgB) 抗体
glycogen branching protein (ECs4277) 抗体
glycogen branching protein (glgB) 抗体
glycogen branching enzyme (glgB) 抗体
1,4-alpha-glucan-branching protein (SCO7332) 抗体
glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase (glgB) 抗体
glycogen branching enzyme (Synpcc7942_1085) 抗体
glycogen branching enzyme (AZC_4116) 抗体
glycogen branching enzyme (Sros_8169) 抗体
glycogen branching enzyme (Despr_0975) 抗体
1,4-alpha-glucan branching enzyme 1 (GBE1) 抗体
glucan (1,4-alpha-), branching enzyme 1 (Gbe1) 抗体
1,4-alpha-glucan branching enzyme 1 (Gbe1) 抗体
2310045H19Rik 抗体
2810426P10Rik 抗体
APBD 抗体
D16Ertd536e 抗体
GBE 抗体
glgBII 抗体
GSD4 抗体
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