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GATM 抗体

(Glycine Amidinotransferase (L-Arginine:glycine Amidinotransferase) (GATM))
This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders. [provided by RefSeq, Jul 2008].

57 results :

GATM 适用: 人, 小鼠, 大鼠 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7262473
 
GATM 适用: 人, 小鼠, 大鼠, 犬, 豚鼠, 马, Cow, 兔, 绵羊, 斑马鱼 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2783416
 
GATM 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7154176
 
GATM 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6140984
 
GATM 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN515955
 
GATM 适用: 人, 小鼠, 大鼠 WB, IHC, IF, IC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7306706
 
GATM 适用: 人, 小鼠, 大鼠 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7247159
 
GATM 适用: 人, 小鼠, 大鼠, 犬, 豚鼠, 马, Bat, Pig, 非洲爪蟾 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6756583
 
GATM 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2H7 unconjugated
产品编号 ABIN515956
 
GATM 适用: 人 WB 宿主: 兔 Polyclonal RB41023 unconjugated
Pubmed 3 references
产品编号 ABIN1881365
 
GATM 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal RB30008 unconjugated
产品编号 ABIN654401
 
GATM 适用: 人 WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro), ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1714621
 
GATM 适用: 人 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1701119
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN5003246
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN5003245
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN1695674
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN1697494
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN1693851
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN1699305
 
GATM 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2813605
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Flow Cytometry (FACS)
    • Immunocytochemistry (ICC)
    • Immunochromatography (IC)
    • Radioimmunoassay (RIA)
  • 适用
    • Human
    • Mouse
    • Rat
    • Dog
    • Guinea Pig
    • Horse
    • All Species
    • Bat
    • Cow
    • Pig
    • Rabbit
    • Sheep
    • Xenopus laevis
    • Zebrafish (Danio rerio)
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 1C9
    • 1E3
    • 2H7
    • RB30008
    • RB41023
  • 抗原表位
    • AA 141-240
    • AA 350-378
    • AA 58-84
    • AA 124-423
    • AA 1-423
    • C-Term
    • N-Term
    • AA 1-100
    • AA 1-279
    • AA 251-300
    • AA 76-423
    • Middle Region
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • APC
    • PE
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1
    • IgG2a
    • IgM kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Signalway
    • Abcepta
    • USBio
    • Abbexa
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • Cohesion Biosciences

Latest Publications for our GATM 抗体

Köttgen, Glazer, Dehghan, Hwang, Katz, Li, Yang, Gudnason, Launer, Harris, Smith, Arking, Astor, Boerwinkle, Ehret, Ruczinski: "Multiple loci associated with indices of renal function and chronic kidney disease." in: Nature genetics, Vol. 41, Issue 6, pp. 712-7, (2010) (PubMed).

Köttgen, Pattaro, Böger, Fuchsberger, Olden, Glazer, Parsa, Gao, Yang, Smith, OConnell, Li, Schmidt, Tanaka, Isaacs, Ketkar, Hwang, Johnson, Dehghan, Teumer, Paré, Atkinson, Zeller, Lohman et al.: "New loci associated with kidney function and chronic kidney disease...." in: Nature genetics, Vol. 42, Issue 5, pp. 376-84, (2010) (PubMed).

Lion-François, Cheillan, Pitelet, Acquaviva-Bourdain, Bussy, Cotton, Guibaud, Gérard, Rivier, Vianey-Saban, Jakobs, Salomons, des Portes: "High frequency of creatine deficiency syndromes in patients with unexplained mental retardation." in: Neurology, Vol. 67, Issue 9, pp. 1713-4, (2006) (PubMed).

Aliases for GATM 抗体

glycine amidinotransferase (L-arginine:glycine amidinotransferase) L homeolog (gatm.L) 抗体
glycine amidinotransferase (GATM) 抗体
glycine amidinotransferase (L-arginine:glycine amidinotransferase) (Gatm) 抗体
glycine amidinotransferase (Gatm) 抗体
glycine amidinotransferase (L-arginine:glycine amidinotransferase) (gatm) 抗体
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