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BCKDHA ELISA试剂盒

(Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Sep 2009].

Active filters:

  • 抗原: BCKDHA
  • Kit
  • 应用范围: ELISA
Catalog no. 产品 适用 宿主 / 克隆类型 应用 价格和交货时间
ABIN5519933
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit 人 –
  • ELISA (ELISA: 有验证图片)
  • 96 tests
发货至: 中国
ABIN1118748
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit 小鼠 –
  • ELISA (ELISA: 所列应用)
  • 96 tests
发货至: 中国
ABIN1118747
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit 人 –
  • ELISA (ELISA: 所列应用)
  • 96 tests
发货至: 中国
ABIN1118746
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit Cow –
  • ELISA (ELISA: 所列应用)
  • 96 tests
发货至: 中国
ABIN1118749
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit 大鼠 –
  • ELISA (ELISA: 所列应用)
  • 96 tests
发货至: 中国
ABIN8089589
BCKDHA ELISA 试剂盒 BCKDHA · ELISA Kit 小鼠 –
  • ELISA (ELISA: 所列应用)
  • 96 tests
发货至: 中国
ELISA Kit
  • ELISA (ELISA: 有验证图片)
适用
人
检测方法
Colorimetric
实验类型
Sandwich ELISA
Detection Range
0.313 ng/mL - 20 ng/mL
样本
Cell Culture Supernatant, Cell Samples, Plasma, Serum, Tissue Lysate
产品编号 ABIN5519933
ELISA Kit
  • ELISA (ELISA: 所列应用)
适用
小鼠
抗原表位
Mitochondrial
检测方法
Colorimetric
产品编号 ABIN1118748
ELISA Kit
  • ELISA (ELISA: 所列应用)
适用
人
抗原表位
Mitochondrial
检测方法
Colorimetric
产品编号 ABIN1118747
ELISA Kit
  • ELISA (ELISA: 所列应用)
适用
Cow
抗原表位
Mitochondrial
检测方法
Colorimetric
产品编号 ABIN1118746
ELISA Kit
  • ELISA (ELISA: 所列应用)
适用
大鼠
抗原表位
Mitochondrial
检测方法
Colorimetric
产品编号 ABIN1118749
ELISA Kit
  • ELISA (ELISA: 所列应用)
适用
小鼠
检测方法
Colorimetric
实验类型
Sandwich ELISA
Detection Range
31.25 pg/mL - 2000 pg/mL
样本
Cell Culture Supernatant, Cell Samples, Plasma, Serum, Tissue Lysate
产品编号 ABIN8089589

Aliases for BCKDHA ELISA试剂盒

2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (LOC704978) ELISA试剂盒
branched chain keto acid dehydrogenase E1, alpha polypeptide (bckdha) ELISA试剂盒
branched chain keto acid dehydrogenase E1, alpha polypeptide (BCKDHA) ELISA试剂盒
2-oxoisovalerate dehydrogenase alpha subunit (branched-chain alpha-keto acid dehydrogenase E1 component alpha chain) (BCKDH E1-alpha) (BCKDE1A) (BckdhA) ELISA试剂盒
branched chain ketoacid dehydrogenase E1, alpha polypeptide (Bckdha) ELISA试剂盒
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