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B3GAT3 抗体

(beta-1,3-Glucuronyltransferase 3 (Glucuronosyltransferase I) (B3GAT3))
The protein encoded by this gene is a member of the glucuronyltransferase gene family, enzymes that exhibit strict acceptor specificity, recognizing nonreducing terminal sugars and their anomeric linkages. This gene product catalyzes the formation of the glycosaminoglycan-protein linkage by way of a glucuronyl transfer reaction in the final step of the biosynthesis of the linkage region of proteoglycans. [provided by RefSeq, Jul 2008].

19 results

B3GAT3 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN565243
 
B3GAT3 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 4C12 unconjugated
产品编号 ABIN525641
 
B3GAT3 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
Pubmed 4 references
产品编号 ABIN525639
 
B3GAT3 适用: 人, Cow, 犬, 马, 小鼠, Pig, 兔, 大鼠, Bat, Hamster, 猴 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6744830
 
B3GAT3 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN525640
 
B3GAT3 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1806095
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal FITC
产品编号 ABIN1969879
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1966097
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN1972135
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal PE
产品编号 ABIN1974467
 
B3GAT3 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN2589630
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2589632
 
B3GAT3 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2589631
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal APC
产品编号 ABIN1963432
 
B3GAT3 适用: 人 WB 宿主: 兔 Polyclonal RB31715 unconjugated
产品编号 ABIN655971
 
B3GAT3 适用: 人, Cow, 犬, 马, 小鼠, Pig, 兔, 大鼠, 山羊, 豚鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2782774
 
B3GAT3 适用: 人 WB, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN950589
 
B3GAT3 适用: 人 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2207613
 
B3GAT3 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1C11 unconjugated
产品编号 ABIN2207614
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Enzyme Immunoassay (EIA)
  • 适用
    • Human
    • Cow
    • Dog
    • Horse
    • Mouse
    • Pig
    • Rabbit
    • Rat
    • Bat
    • Goat
    • Guinea Pig
    • Hamster
    • Monkey
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 1C11
    • 4C12
    • RB31715
  • 抗原表位
    • AA 293-321
    • AA 1-335
    • C-Term
    • AA 236-335
    • AA 300-329
    • AA 236-336
    • AA 35-84
    • N-Term
  • 标记
    • 非结合性
    • APC
    • Biotin
    • FITC
    • HRP
    • PE
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG2a kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • USBio
    • Abcepta
    • Acris
    • Aviva Systems Biology

Latest Publications for our B3GAT3 抗体

Job, Mizumoto, Smith, Couser, Brazil, Saal, Patterson, Gibson, Soden, Miller, Thiffault, Saunders, Yamada, Hoffmann, Sugahara, Farrow: "Functional validation of novel compound heterozygous variants in B3GAT3 resulting in severe osteopenia and fractures: expanding the disease phenotype." in: BMC medical genetics, Vol. 17, Issue 1, pp. 86, (2016) (PubMed).

Budde, Mizumoto, Kogawa, Becker, Altmüller, Thiele, Rüschendorf, Toliat, Kaleschke, Hämmerle, Höhne, Sugahara, Nürnberg, Kennerknecht: "Skeletal dysplasia in a consanguineous clan from the island of Nias/Indonesia is caused by a novel mutation in B3GAT3." in: Human genetics, Vol. 134, Issue 7, pp. 691-704, (2015) (PubMed).

Baasanjav, Al-Gazali, Hashiguchi, Mizumoto, Fischer, Horn, Seelow, Ali, Aziz, Langer, Saleh, Becker, Nürnberg, Cantagrel, Gleeson, Gomez, Michel, Stricker, Lindner, Nürnberg, Sugahara, Mundlos et al.: "Faulty initiation of proteoglycan synthesis causes cardiac and joint defects. ..." in: American journal of human genetics, Vol. 89, Issue 1, pp. 15-27, (2011) (PubMed).

Hiyama, Gajghate, Sakai, Mochida, Shapiro, Risbud: "Activation of TonEBP by calcium controls {beta}1,3-glucuronosyltransferase-I expression, a key regulator of glycosaminoglycan synthesis in cells of the intervertebral disc." in: The Journal of biological chemistry, Vol. 284, Issue 15, pp. 9824-34, (2009) (PubMed).

Aliases for B3GAT3 抗体

beta-1,3-glucuronyltransferase 3 (B3GAT3) 抗体
beta-1,3-glucuronyltransferase 3 (glucuronosyltransferase I) (B3gat3) 抗体
beta-1,3-glucuronyltransferase 3 (B3gat3) 抗体
2810405M13Rik 抗体
Glcat-i 抗体
GLCATI 抗体
GlcUAT-I 抗体
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