SGSH 抗体 (C-Term)
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Quick Overview for SGSH 抗体 (C-Term) (ABIN954998)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 427-457, C-Term
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特异性
- Recognizes Sulphamidase / SGSH (C-term).
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纯化方法
- Protein A column followed by peptide Affinity purification
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免疫原
- KLH conjugated synthetic peptide between 427~457 amino acids from the C-terminal region of Human SGSH. Genename: SGSH
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亚型
- Ig Fraction
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.25 mg/mL
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缓冲液
- PBS with 0.09 % (W/V) Sodium Azide as preservative
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储存液
- Sodium azide
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注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid repeated freezing and thawing.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- Sulphamidase / SGSH
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背景
- SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.Synonyms: HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase
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基因ID
- 6448
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NCBI登录号
- NP_000190
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途径
- Glycosaminoglycan Metabolic Process
抗原
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