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AGLU 抗体 (N-Term)

AGLU 适用: 人 WB, EIA, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN950380
发货至: 中国
  • 抗原 See all AGLU 抗体
    AGLU (alpha-Glucosidase (AGLU))
    抗原表位
    AA 173-203, N-Term
    适用
    • 6
    • 5
    宿主
    • 8
    • 3
    克隆类型
    • 8
    • 3
    多克隆
    标记
    • 8
    • 3
    This AGLU antibody is un-conjugated
    应用范围
    • 10
    • 4
    • 4
    • 4
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    Western Blotting (WB), Enzyme Immunoassay (EIA), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    特异性
    This antibody recognizes Human Alpha-glucosidase (N-term).
    纯化方法
    Protein A column, followed by peptide affinity purification
    免疫原
    conjugated synthetic peptide between 173-203 amino acids from the N-terminal region of Human Alpha-glucosidase Genename: GAA
    亚型
    Ig Fraction
    Top Product
    Discover our top product AGLU Primary Antibody
  • 应用备注
    Optimal working dilution should be determined by the investigator.
    限制
    仅限研究用
  • 状态
    Liquid
    浓度
    0.25 mg/mL
    缓冲液
    PBS containing 0.09 % (W/V) Sodium Azide as preservative
    储存液
    Sodium azide
    注意事项
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    注意事项
    Avoid repeated freezing and thawing.
    储存条件
    4 °C/-20 °C
    储存方法
    Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
  • 抗原
    AGLU (alpha-Glucosidase (AGLU))
    别名
    alpha-Glucosidase (AGLU 产品)
    别名
    MG antibody, MGA antibody, SPAC56F8.01 antibody, SPAC922.02c antibody, CG11909 antibody, CT33098 antibody, Dmel\\CG11909 antibody, GB19017 antibody, 6030407P20Rik antibody, maltase-glucoamylase antibody, alpha-glucosidase (predicted) antibody, alpha-glucosidase antibody, glucosidase, alpha, acid antibody, target of brain insulin antibody, sucrase-isomaltase antibody, MGAM antibody, SPAC30D11.01c antibody, LMOf2365_0194 antibody, SPAC1039.11c antibody, Gaa antibody, tobi antibody, SI antibody, Hbg3 antibody, Mgam antibody
    背景
    This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.Synonyms: Acid maltase, Aglucosidase alfa, GAA, LYAG, Lysosomal alpha-glucosidase
    分子量
    105319 Da
    基因ID
    2548
    NCBI登录号
    NP_000143
    途径
    Cellular Glucan Metabolic Process
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