AGLU 抗体 (N-Term)
Quick Overview for AGLU 抗体 (N-Term) (ABIN950380)
抗原
See all AGLU 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 173-203, N-Term
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特异性
- This antibody recognizes Human Alpha-glucosidase (N-term).
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纯化方法
- Protein A column, followed by peptide affinity purification
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免疫原
- conjugated synthetic peptide between 173-203 amino acids from the N-terminal region of Human Alpha-glucosidase Genename: GAA
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亚型
- Ig Fraction
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anti-alpha-Glucosidase (AGLU) (AA 213-392) antibody
AGLU 适用: 人 WB, IP, IHC, ICC 宿主: 兔 Polyclonal unconjugated
anti-alpha-Glucosidase (AGLU) antibodyAGLU 适用: 人 WB 宿主: 小鼠 Monoclonal 43G7 unconjugated
anti-alpha-Glucosidase (AGLU) (AA 860-1090) antibodyAGLU 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.25 mg/mL
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缓冲液
- PBS containing 0.09 % (W/V) Sodium Azide as preservative
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储存液
- Sodium azide
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注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid repeated freezing and thawing.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
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- AGLU (alpha-Glucosidase (AGLU))
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别名
- alpha-Glucosidase
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背景
- This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.Synonyms: Acid maltase, Aglucosidase alfa, GAA, LYAG, Lysosomal alpha-glucosidase
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分子量
- 105319 Da
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基因ID
- 2548
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NCBI登录号
- NP_000143
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途径
- Cellular Glucan Metabolic Process
抗原
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