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AGLU 抗体 (N-Term)

This anti-AGLU antibody is a 兔 多克隆 antibody detecting AGLU in WB, EIA 和 IHC (p). Suitable for 人.
产品编号 ABIN950380
发货至: 中国
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Quick Overview for AGLU 抗体 (N-Term) (ABIN950380)

抗原

See all AGLU 抗体
AGLU (alpha-Glucosidase (AGLU))

适用

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宿主

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克隆类型

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多克隆

标记

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This AGLU antibody is un-conjugated

应用范围

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Western Blotting (WB), Enzyme Immunoassay (EIA), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
  • 抗原表位

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    AA 173-203, N-Term

    特异性

    This antibody recognizes Human Alpha-glucosidase (N-term).

    纯化方法

    Protein A column, followed by peptide affinity purification

    免疫原

    conjugated synthetic peptide between 173-203 amino acids from the N-terminal region of Human Alpha-glucosidase Genename: GAA

    亚型

    Ig Fraction
  • 应用备注

    Optimal working dilution should be determined by the investigator.

    限制

    仅限研究用
  • 状态

    Liquid

    浓度

    0.25 mg/mL

    缓冲液

    PBS containing 0.09 % (W/V) Sodium Azide as preservative

    储存液

    Sodium azide

    注意事项

    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    注意事项

    Avoid repeated freezing and thawing.

    储存条件

    4 °C/-20 °C

    储存方法

    Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
  • 抗原

    AGLU (alpha-Glucosidase (AGLU))

    别名

    alpha-Glucosidase

    背景

    This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.Synonyms: Acid maltase, Aglucosidase alfa, GAA, LYAG, Lysosomal alpha-glucosidase

    分子量

    105319 Da

    基因ID

    2548

    NCBI登录号

    NP_000143

    途径

    Cellular Glucan Metabolic Process
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