PEX19 抗体 (C-Term)
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Quick Overview for PEX19 抗体 (C-Term) (ABIN926758)
抗原
See all PEX19 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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纯化方法
- Purified
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免疫原
- PEX19 antibody was raised in rabbit using the C terminal of PEX19 as the immunogen
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应用备注
- Optimal conditions should be determined by the investigator.
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说明
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PEX19 Blocking Peptide, (ABIN936282), is also available for use as a blocking control in assays to test for specificity of this PEX19 antibody
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限制
- 仅限研究用
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状态
- Lyophilized
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浓度
- Lot specific
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缓冲液
- Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.
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注意事项
- Avoid repeated freeze/thaw cycles.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store at 4 °C, following reconstitution, aliquot and store at -20 °C.
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- PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))
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别名
- PEX19
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背景
- This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. Synonyms: Polyclonal PEX19 antibody, Anti-PEX19 antibody, peroxisomal biogenesis factor 19 antibody, D1S2223E antibody, FLJ55296 antibody, HK33 antibody, PMP1 antibody, PMPI antibody, PXF antibody, PXMP1 antibody.
抗原
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