GLA 抗体 (AA 101-200) (HRP)
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北京 101111
Quick Overview for GLA 抗体 (AA 101-200) (HRP) (ABIN898235)
抗原
See all GLA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 101-200
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交叉反应
- 人, 小鼠, 大鼠
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预测反应
- Dog,Cow,Pig,Rabbit
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纯化方法
- Purified by Protein A.
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免疫原
- KLH conjugated synthetic peptide derived from human Galactosidase alpha
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亚型
- IgG
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anti-Galactosidase, alpha (GLA) (AA 81-429) antibody
GLA 适用: 人 WB, IHC, IP, ICC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 81-429) antibodyGLA 适用: 人 WB, IHC 宿主: 小鼠 Monoclonal C8 unconjugated
anti-Galactosidase, alpha (GLA) antibodyKO Validated GLA 适用: 人 WB, IP, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 1-80) antibodyGLA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) antibodyKD Validated GLA 适用: 人 WB, ICC, FACS 宿主: 兔 Monoclonal 23GB5545 unconjugated Recombinant Antibody
anti-Galactosidase, alpha (GLA) (AA 147-371) antibodyGLA 适用: 人 WB, IHC, IP, ICC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 1-429) antibodyGLA 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 83-112), (N-Term) antibodyGLA 适用: 人 WB, FACS, IF, IHC (p) 宿主: 兔 Polyclonal RB19115 unconjugated
anti-Galactosidase, alpha (GLA) (AA 101-200) antibodyGLA 适用: 人, 小鼠, 大鼠 WB, ELISA, FACS, IHC (p), IF (cc), IF (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 150-429) antibodyGLA 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
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应用备注
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WB 1:300-5000
IHC-P 1:200-400
IHC-F 1:100-500 -
限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 μg/μL
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缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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注意事项
- Do NOT add Sodium Azide! Use of Sodium Azide will inhibit enzyme activity of horseradish peroxidase.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
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有效期
- 12 months
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- GLA (Galactosidase, alpha (GLA))
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别名
- Galactosidase alpha
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背景
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Synonyms: GALA, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Melibiase, GLA
Background: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.
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基因ID
- 2717
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UniProt
- P06280
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途径
- SARS-CoV-2 Protein Interactome
抗原
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