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GLA 抗体 (AA 101-200)

Name: GLA 抗体 (AA 101-200)
SKU: ABIN872875
Availability: OutOfStock

This anti-GLA antibody is a 兔多克隆 antibody detecting GLA in WB, ELISA, FACS, IHC (p), IF (cc), IF (p) 和 IHC (fro). Suitable for 人, 小鼠和大鼠.

Formalin-fixed and paraffin embedded human rectal carcinoma labeled with Anti-Galactosidase alpha Polyclonal Antibody, Unconjugated (ABIN872875) at 1:200 followed by conjugation to the secondary antibody and DAB staining. (GLA 抗体 (AA 101-200))

IHC

Lane 1: mouse liver lysates Lane 2: human colon carcinoma lysates probed with Anti Galactosidase alpha Polyclonal Antibody, Unconjugated (ABIN872875) at 1:200 in 4 °C. (GLA 抗体 (AA 101-200))

SDS

2 images

产品编号 ABIN872875

发货至: 中国

Quick Overview for GLA 抗体 (AA 101-200) (ABIN872875)

抗原

See all GLA 抗体

GLA (Galactosidase, alpha (GLA))

适用

人, 小鼠, 大鼠

宿主

兔

克隆类型

多克隆

标记

This GLA antibody is un-conjugated

应用范围

Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Frozen Sections) (IHC (fro))

Discover our top product GLA Primary Antibody

抗原表位
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12

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2

2

2

1

1

1
AA 101-200

交叉反应

人, 小鼠, 大鼠

预测反应

Dog,Cow,Pig,Rabbit

纯化方法

Purified by Protein A.

免疫原

KLH conjugated synthetic peptide derived from human Galactosidase alpha

亚型

IgG
anti-Galactosidase, alpha (GLA) (AA 81-429) antibody
GLA 适用: 人 WB, IHC, IP, FACS, ICC 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 81-429) antibody
GLA 适用: 人 WB, IHC 宿主: 小鼠 Monoclonal C8 unconjugated

anti-Galactosidase, alpha (GLA) antibody
KO Validated GLA 适用: 人 WB, IP, IHC (p) 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 1-80) antibody
GLA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 147-371) antibody
GLA 适用: 人 WB, IHC, IP, FACS, ICC 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 1-429) antibody
GLA 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 83-112), (N-Term) antibody
GLA 适用: 人 WB, FACS, IF, IHC (p) 宿主: 兔 Polyclonal RB19115 unconjugated

anti-Galactosidase, alpha (GLA) (AA 32-429) antibody
GLA 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 1-429) antibody
GLA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated

anti-Galactosidase, alpha (GLA) (AA 150-429) antibody
GLA 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated

应用备注

WB 1:300-5000
ELISA 1:500-1000
FCM 1:20-100
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

限制

仅限研究用
状态

Liquid

浓度

1 μg/μL

缓冲液

0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.

储存液

ProClin

注意事项

This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

储存条件

4 °C,-20 °C

储存方法

Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.

有效期

12 months
抗原

GLA (Galactosidase, alpha (GLA))

别名

Galactosidase alpha

背景

Synonyms: GALA, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Melibiase, GLA
Background: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

基因ID

2717

UniProt

P06280

途径

SARS-CoV-2 Protein Interactome