NPHP1 抗体 (AA 510-590)
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北京 101111
Quick Overview for NPHP1 抗体 (AA 510-590) (ABIN8123264)
抗原
See all NPHP1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 510-590
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原理
- NPHP1 Antibody
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特异性
- NPHP1 Polyclonal Antibody detects endogenous levels of protein.
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纯化方法
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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免疫原
- Synthesized peptide derived from human protein . at AA range: 510-590
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亚型
- IgG
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anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 345-614) antibody
NPHP1 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-121) antibodyNPHP1 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibodyNPHP1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-109) antibodyNPHP1 适用: 人 ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibodyNPHP1 适用: 人, 小鼠, 大鼠 WB, IF 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibodyNPHP1 适用: 人 WB 宿主: 兔 Monoclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 467-516) antibodyNPHP1 适用: 人, 小鼠, 大鼠, 犬, Cow, 豚鼠, 马, Pig, 兔, Bat, 猴, 非洲爪蟾 WB 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibody (Biotin)NPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal Biotin
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibody (FITC)NPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal FITC
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-109) antibodyNPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
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应用备注
- WB 1:500-2000 ELISA 1:5000-20000
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Liquid in PBS containing 50 % glycerol, and 0.02 % sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C/1 year
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有效期
- 12 months
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- NPHP1 (Nephronophthisis 1 (Juvenile) (NPHP1))
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别名
- NPHP1
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背景
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Background: This gene encodes a protein with src homology domain 3 (SH3) patterns. This protein interacts with Crk-associated substrate, and it appears to function in the control of cell division, as well as in cell-cell and cell-matrix adhesion signaling, likely as part of a multifunctional complex localized in actin- and microtubule-based structures. Mutations in this gene cause familial juvenile nephronophthisis type 1, a kidney disorder involving both tubules and glomeruli. Defects in this gene are also associated with Senior-Loken syndrome type 1, also referred to as juvenile nephronophthisis with Leber amaurosis, which is characterized by kidney and eye disease, and with Joubert syndrome type 4, which is characterized by cerebellar ataxia, oculomotor apraxia, psychomotor delay and neonatal breathing abnormalities, sometimes including retinal dystrophy and renal disease. Multiple transcript variants encoding diffe
Gene Name: NPHP1 NPH1
Protein Name: Nephrocystin-1 (Juvenile nephronophthisis 1 protein)
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基因ID
- 4867
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UniProt
- O15259
抗原
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