SGSH 抗体
Our Local Distributor
北京 101111
Quick Overview for SGSH 抗体 (ABIN8123211)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
克隆位点
-
-
原理
- SGSH Rabbit mAb
-
特异性
- This antibody detects endogenous levels of SGSH protein.
-
纯化方法
- The antibody was purified by protein A affinity chromatography.
-
免疫原
- Recombinant protein (or fragment).
-
亚型
- IgG
-
-
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 21-389) antibody
SGSH 适用: 人 WB, IHC, ICC, IF 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (C-Term) antibodySGSH 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 301-388) antibodySGSH 适用: 人 WB, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 420-449), (C-Term) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal RB24406 unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
-
-
应用备注
- WB, 1:1000-1:5000 | IHC, 1:100-1:300 | IF, 1:100-1:300 |
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
缓冲液
- The antibody is provided in liquid form in phosphate - buffered saline with 50 % glycerol, 0.05 % BSA, and 0.05 % Proclin 300.
-
储存液
- ProClin
-
注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
注意事项
- Avoid freeze / thaw cycles
-
储存条件
- -20 °C
-
储存方法
- Store at-20°C. Avoid freeze / thaw cycles.
-
-
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
-
别名
- SGSH
-
背景
-
Synonyms: SGSH, HSS, N-sulphoglucosamine sulphohydrolase , Sulfoglucosamine sulfamidase, Sulphamidase,
Background: This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
Gene Name: SGSH, HSS
Protein Name: SGSH
-
基因ID
- 6448
-
UniProt
- P51688
-
途径
- Glycosaminoglycan Metabolic Process
抗原
-
