CLCN1 抗体
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北京 101111
Quick Overview for CLCN1 抗体 (ABIN8120516)
抗原
See all CLCN1 抗体适用
宿主
克隆类型
标记
应用范围
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原理
- CLCN1 Antibody
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特异性
- CLCN1 Polyclonal Antibody detects endogenous levels of protein.
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纯化方法
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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免疫原
- Synthesized peptide derived from part region of human protein
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亚型
- IgG
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应用备注
- WB 1:500-2000 ELISA 1:5000-20000
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Liquid in PBS containing 50 % glycerol, and 0.02 % sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C/1 year
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有效期
- 12 months
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- CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))
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别名
- CLCN1
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背景
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Background: chloride voltage-gated channel 1(CLCN1) Homo sapiens The CLCN family of voltage-dependent chloride channel genes comprises nine members (CLCN1-7, Ka and Kb) which demonstrate quite diverse functional characteristics while sharing significant sequence homology.The protein encoded by this gene regulates the electric excitability of the skeletal muscle membrane. Mutations in this gene cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants. [provided by RefSeq, Mar 2012],
Gene Name: CLCN1 CLC1
Protein Name: Chloride channel protein 1 (ClC-1) (Chloride channel protein, skeletal muscle)
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基因ID
- 1180
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UniProt
- P35523
抗原
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