HMBS 抗体 (C-Term)
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北京 101111
Quick Overview for HMBS 抗体 (C-Term) (ABIN8102862)
抗原
See all HMBS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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原理
- HMBS Antibody - C-terminal region
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序列
- VPAQHEDGPE DDPQLVGITA RNIPRGPQLA AQNLGISLAN LLLSKGAKNI
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纯化方法
- Affinity Purified
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免疫原
- The immunogen is a synthetic peptide directed towards the C-terminal region of Human HEM3
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应用备注
- Optimal working dilution should be determined by the investigator.
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说明
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP74562-100UG
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.5 mg/mL
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缓冲液
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- prevent freeze-thaw cycles
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储存条件
- 4 °C,-20 °C
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储存方法
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- HMBS (Hydroxymethylbilane Synthase (HMBS))
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别名
- HMBS
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背景
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Background Information: This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Gene Name: hydroxymethylbilane synthase
Alternative Symbols: UPS, PBGD, PORC, PBG-D
Protein Name: porphobilinogen deaminase
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分子量
- 39kDa
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基因ID
- 3145
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UniProt
- P08397
抗原
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