SGSH 抗体 (AA 206-502) (FITC)
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北京 101111
Quick Overview for SGSH 抗体 (AA 206-502) (FITC) (ABIN8013233)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 206-502
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原理
- Anti-HSS/SGSH Antibody FITC Conjugated
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交叉反应 （详细）
- No cross-reactivity with other proteins.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human HSS/SGSH recombinant protein (Position: R206-L502).
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亚型
- IgG
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anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 21-389) antibody
SGSH 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (C-Term) antibodySGSH 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 301-388) antibodySGSH 适用: 人 WB, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 420-449), (C-Term) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal RB24406 unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (N-Term) antibodySGSH 适用: 人, 小鼠, 大鼠, Cow, 马, 犬, Pig, 豚鼠 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Flow Cytometry, Optimal dilutions should be determined by end users.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Each vial contains 50 % glycerol, 0.9 % NaCl, 0.2 % Na2HPO4, 0.02 % Sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- At -20°C for one year from date of receipt. Avoid repeated freezing and thawing. Protect from light.
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有效期
- 12 months
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH
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背景
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Background: N-sulphoglucosamine sulphohydrolase is an enzyme that in humans is encoded by the SGSH gene. This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Gene Full Name: N-sulfoglucosamine sulfohydrolase
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基因ID
- 6448
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UniProt
- P51688
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途径
- Glycosaminoglycan Metabolic Process
抗原
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