GLA 抗体 (AA 83-112)
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北京 101111
Quick Overview for GLA 抗体 (AA 83-112) (ABIN7876930)
抗原
See all GLA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 83-112
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原理
- Galactosidase alpha Antibody / Gla
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纯化方法
- Purified
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免疫原
- A portion of amino acids 83-112 from the human protein was used as the immunogen for the Galactosidase alpha antibody.
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亚型
- Ig Fraction
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应用备注
- The stated application concentrations are suggested starting points. Titration of the Galactosidase alpha antibody may be required due to differences in protocols and secondary/substrate sensitivity.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- In 1X PBS, pH 7.4, with 0.09 % sodium azide
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Aliquot the Galactosidase alpha antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.
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- GLA (Galactosidase, alpha (GLA))
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别名
- Galactosidase alpha
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背景
- GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
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UniProt
- P06280
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途径
- SARS-CoV-2 Protein Interactome
抗原
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