GALNS 抗体 (AA 236-263)
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北京 101111
Quick Overview for GALNS 抗体 (AA 236-263) (ABIN7872630)
抗原
See all GALNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 236-263
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原理
- GALNS Antibody
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纯化方法
- Antigen affinity purified
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免疫原
- A portion of amino acids 236-263 from the human protein was used as the immunogen for the GALNS antibody.
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亚型
- Ig Fraction
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应用备注
- The stated application concentrations are suggested starting points. Titration of the GALNS antibody may be required due to differences in protocols and secondary/substrate sensitivity.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- In 1X PBS, pH 7.4, with 0.09 % sodium azide
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Aliquot the GALNS antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.
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- GALNS (Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))
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别名
- GALNS
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背景
- This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. [provided by RefSeq].
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UniProt
- P34059
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途径
- Glycosaminoglycan Metabolic Process
抗原
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