SGSH 抗体 (AA 206-502)
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Quick Overview for SGSH 抗体 (AA 206-502) (ABIN7872102)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 206-502
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原理
- SGSH Antibody / N-sulphoglucosamine sulphohydrolase / HSS
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纯化方法
- Antigen affinity purified
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免疫原
- E. coli-derived recombinant human protein (amino acids R206-L502) was used as the immunogen for the SGSH antibody.
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亚型
- IgG
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应用备注
- Optimal dilution of the SGSH antibody should be determined by the researcher.
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限制
- 仅限研究用
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状态
- Lyophilized
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缓冲液
- 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water
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储存条件
- 4 °C,-20 °C
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储存方法
- After reconstitution, the SGSH antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH
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背景
- N-sulphoglucosamine sulphohydrolase is an enzyme that in humans is encoded by the SGSH gene. This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
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UniProt
- P51688
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途径
- Glycosaminoglycan Metabolic Process
抗原
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