POMGNT1 抗体 (AA 96-394)
Quick Overview for POMGNT1 抗体 (AA 96-394) (ABIN7602699)
抗原
See all POMGNT1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 96-394
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原理
- Anti-POMGNT1 Antibody Picoband®
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产品特性
- Anti-POMGNT1 Antibody Picoband® (ABIN7602699). Tested in WB, IHC, Flow Cytometry, ELISA applications. This antibody reacts with Human, Mouse, Rat. The brand Picoband indicates this is a premium antibody that guarantees superior quality, high affinity, and strong signals with minimal background in Western blot applications. Only our best-performing antibodies are designated as Picoband, ensuring unmatched performance.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human POMGNT1 recombinant protein (Position: R96-E394). Human POMGNT1 shares 99.7% amino acid (aa) sequence identity with both mouse and rat POMGNT1.
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anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) (AA 411-660) antibody
POMGNT1 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) antibodyPOMGNT1 适用: 人, 小鼠, 大鼠 ELISA, WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) (AA 221-318) antibodyPOMGNT1 适用: 人 ELISA, WB, IHC (p) 宿主: 小鼠 Monoclonal 6C12 unconjugated
anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) (AA 59-300) antibodyPOMGNT1 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) (AA 221-319) antibodyPOMGNT1 适用: 人 ELISA, WB, IHC, IHC (p) 宿主: 小鼠 Monoclonal 6C12 unconjugated
anti-Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1) (AA 47-96) antibodyPOMGNT1 适用: 人, 小鼠, 大鼠, Cow, 马, 兔, Hamster, 猴 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
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Western blot, 0.1-0.25 μg/mL, Human, Mouse, Rat
Immunohistochemistry, 2-5 μg/mL, Mouse, Rat
Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human
ELISA, 0.1-0.5 μg/mL, -
1. Biancheri, R., Bertini, E., Falace, A., Pedemonte, M., Rossi, A., D'Amico, A., Scapolan, S., Bergamino, L., Petrini, S., Cassandrini, D., Broda, P., Manfredi, M., Zara, F., Santorelli, F. M., Minetti, C., Bruno, C. POMGnT1 mutations in congenital muscular dystrophy: genotype-phenotype correlation and expanded clinical spectrum. Arch. Neurol. 63: 1491-1495, 2006. 2. Bouchet, C., Gonzales, M., Vuillaumier-Barrot, S., Devisme, L., Lebizec, C., Alanio, E., Bazin, A., Bessieres-Grattagliano, B., Bigi, N., Blanchet, P., Bonneau, D., Bonnieres, M., and 22 others. Molecular heterogeneity in fetal forms of type II lissencephaly. Hum. Mutat. 28: 1020-1027, 2007. 3. Clement, E. M., Godfrey, C., Tan, J., Brockington, M., Torelli, S., Feng, L., Brown, S. C., Jimenez-Mallebrera, C., Sewry, C. A., Longman, C., Mein, R., Abbs, S., Vajsar, J., Schachter, H., Muntoni, F. Mild POMGnT1 mutations underlie a novel limb-girdle muscular dystrophy variant. Arch. Neurol. 65: 137-141, 2008. -
限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing.
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- POMGNT1 (Protein O-Linked Mannose Beta1,2-N-Acetylglucosaminyltransferase (POMGNT1))
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别名
- POMGNT1
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背景
- Protein O-linked-mannose beta-1,2-N-acetylglucosaminyltransferase 1 is an enzyme that in humans is encoded by the POMGNT1 gene. This gene encodes a type II transmembrane protein that resides in the Golgi apparatus. It participates in O-mannosyl glycosylation and is specific for alpha linked terminal mannose. Mutations in this gene may be associated with muscle-eye-brain disease and several congenital muscular dystrophies. Alternatively spliced transcript variants that encode different protein isoforms have been described.
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分子量
- 75 kDa
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基因ID
- 55624
抗原
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