MCCC1 抗体 (AA 104-715)
Quick Overview for MCCC1 抗体 (AA 104-715) (ABIN7599657)
抗原
See all MCCC1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 104-715
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原理
- Anti-MCCC1 Antibody Picoband®
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交叉反应 （详细）
- No cross-reactivity with other proteins.
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产品特性
- Anti-MCCC1 Antibody Picoband® (ABIN7599657). Tested in ELISA, IF, IHC, ICC, WB applications. This antibody reacts with Human, Mouse, Rat. The brand Picoband indicates this is a premium antibody that guarantees superior quality, high affinity, and strong signals with minimal background in Western blot applications. Only our best-performing antibodies are designated as Picoband, ensuring unmatched performance.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human MCCC1 recombinant protein (Position: Q104-E715).
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亚型
- IgG
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anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 526-725) antibody
MCCC1 适用: 人 ELISA, IHC, IP 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 526-725) antibodyMCCC1 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) antibodyMCCC1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 526-625) antibodyMCCC1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2G8 unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) antibodyMCCC1 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 1-200) antibodyMCCC1 适用: 人 ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 1-725) antibodyMCCC1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) (AA 484-717) antibodyMCCC1 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
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应用备注
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Western blot, 0.25-0.5 μg/mL, Human, Mouse, Rat
Immunohistochemistry, 2-5 μg/mL, Human
Immunocytochemistry/Immunofluorescence, 5 μg/mL, Human
ELISA, 0.1-0.5 μg/mL, -
1. Baumgartner, M. R., Almashanu, S., Suormala, T., Obie, C., Cole, R. N., Packman, S., Baumgartner, E. R., Valle, D. The molecular basis of human 3-methylcrotonyl-CoA carboxylase deficiency. J. Clin. Invest. 107: 495-504, 2001. 2. Baumgartner, M. R., Dantas, M. F., Suormala, T., Almashanu, S., Giunta, C., Friebel, D., Gebhardt, B., Fowler, B., Hoffmann, G. F., Baumgartner, E. R., Valle, D. Isolated 3-methylcrotonyl-CoA carboxylase deficiency: evidence for an allele-specific dominant negative effect and responsiveness to biotin therapy. Am. J. Hum. Genet. 75: 790-800, 2004. 3. Gallardo, M. E., Desviat, L. R., Rodriguez, J. M., Esparza-Gordillo, J., Perez-Cerda, C., Perez, B., Rodriguez-Pombo, P., Criado, O., Sanz, R., Morton, D. H., Gibson, K. M., Le, T. P., Ribes, A., Rodriguez de Cordoba, S., Ugarte, M., Penalva, M. A. The molecular basis of 3-methylcrotonylglycinuria, a disorder of leucine catabolism. Am. J. Hum. Genet. 68: 334-346, 2001. -
限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing.
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- MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
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别名
- MCCC1
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背景
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Synonyms: BAG family molecular chaperone regulator 5,BAG-5,Bcl-2-associated athanogene 5,BAG5,KIAA0873,
Tissue Specificity: Expressed in all tissues examined with lower levels in brain and testis.
Background: This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
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分子量
- 80 kDa
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基因ID
- 56922
抗原
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