IDUA 抗体 (AA 1-87)
Quick Overview for IDUA 抗体 (AA 1-87) (ABIN7599565)
抗原
See all IDUA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1-87
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原理
- Anti-IDUA Antibody Picoband®
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交叉反应 （详细）
- No cross reactivity with other proteins.
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产品特性
- Anti-IDUA Antibody Picoband® (ABIN7599565). Tested in ELISA, IF, IHC, WB, Flow Cytometry applications. This antibody reacts with Human, Mouse, Rat. The brand Picoband indicates this is a premium antibody that guarantees superior quality, high affinity, and strong signals with minimal background in Western blot applications. Only our best-performing antibodies are designated as Picoband, ensuring unmatched performance.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human INSIG1 recombinant protein (Position: M1-R87).
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亚型
- IgG
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anti-Iduronidase, alpha-L- (IDUA) (AA 236-264) antibody
IDUA 适用: 人 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB26860 unconjugated
anti-Iduronidase, alpha-L- (IDUA) (AA 28-306) antibodyIDUA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Iduronidase, alpha-L- (IDUA) (AA 28-653) antibodyIDUA 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Iduronidase, alpha-L- (IDUA) antibodyIDUA 适用: 人, 小鼠 ELISA, WB 宿主: 兔 Polyclonal unconjugated
anti-Iduronidase, alpha-L- (IDUA) antibodyIDUA 适用: 人, 小鼠 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Iduronidase, alpha-L- (IDUA) (AA 101-200) antibodyIDUA 适用: 大鼠 ELISA, WB 宿主: 兔 Polyclonal unconjugated
anti-Iduronidase, alpha-L- (IDUA) (AA 121-170) antibodyIDUA 适用: 人, 小鼠, 豚鼠, 马, Cow, Hamster WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
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应用备注
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Western blot, 0.25-0.5 μg/mL, Human, Mouse, Rat
Immunohistochemistry, 2-5 μg/mL, Human, Mouse, Rat
Immunofluorescence, 5 μg/mL, Human
Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human
ELISA, 0.1-0.5 μg/mL, -
1. Alif, N., Hess, K., Straczek, J., Sebbar, S., N'Bou, A., Nabet, P., Dousset, B. Mucopolysaccharidosis type I: characterization of a common mutation that causes Hurler syndrome in Moroccan subjects. Ann. Hum. Genet. 63: 9-16, 1999. 2. Aronovich, E. L., Pan, D., Whitley, C. B. Molecular genetic defect underlying alpha-L-iduronidase pseudodeficiency. Am. J. Hum. Genet. 58: 75-85, 1996. 3. Ashton, L. J., Brooks, D. A., McCourt, P. A. G., Muller, V. J., Clements, P. R., Hopwood, J. J. Immunoquantification and enzyme kinetics of alpha-L-iduronidase in cultured fibroblasts from normal controls and mucopolysaccharidosis type I patients. Am. J. Hum. Genet. 50: 787-794, 1992. -
限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing.
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- IDUA (Iduronidase, alpha-L- (IDUA))
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别名
- IDUA
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背景
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Synonyms: 70 kDa ribosomal protein S6 kinase 1 antibody, KS6B1_HUMAN antibody, p70 alpha antibody, P70 beta 1 antibody, p70 ribosomal S6 kinase alpha antibody, p70 ribosomal S6 kinase beta 1 antibody, p70 S6 kinase alpha antibody, P70 S6 Kinase antibody, p70 S6 kinase alpha 1 antibody, p70 S6 kinase alpha 2 antibody, p70 S6K antibody, p70 S6K-alpha antibody, p70 S6KA antibody, p70(S6K) alpha antibody, p70(S6K)-alpha antibody, p70-alpha antibody, p70-S6K 1 antibody, p70-S6K antibody, P70S6K antibody, P70S6K1 antibody, p70S6Kb antibody, PS6K antibody, Ribosomal protein S6 kinase 70 kDa polypeptide 1 antibody, Ribosomal protein S6 kinase beta 1 antibody, Ribosomal protein S6 kinase beta-1 antibody, Ribosomal protein S6 kinase I antibody, RPS6KB1 antibody, S6K antibody, S6K-beta-1 antibody, S6K1 antibody, Serine/threonine kinase 14 alpha antibody, Serine/threonine-protein kinase 14A antibody, STK14A antibody
Tissue Specificity: Expressed in all tissues.
Background: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
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分子量
- 73 kDa
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基因ID
- 3425
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UniProt
- P35475
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途径
- Glycosaminoglycan Metabolic Process
抗原
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