FAH 抗体 (AA 1-342)
Quick Overview for FAH 抗体 (AA 1-342) (ABIN7599291)
抗原
See all FAH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1-342
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原理
- Anti-FAA/FAH Antibody Picoband®
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交叉反应 （详细）
- No cross-reactivity with other proteins.
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产品特性
- Anti-FAA/FAH Antibody Picoband® (ABIN7599291). Tested in ELISA, Flow Cytometry, IHC, WB applications. This antibody reacts with Human, Mouse, Rat. The brand Picoband indicates this is a premium antibody that guarantees superior quality, high affinity, and strong signals with minimal background in Western blot applications. Only our best-performing antibodies are designated as Picoband, ensuring unmatched performance.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human FAA/FAH recombinant protein (Position: M1-P342).
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亚型
- IgG
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anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (C-Term) antibody
FAH 适用: 人, 小鼠, 大鼠, 犬, 马, Cow, 豚鼠, 兔, 斑马鱼 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) antibodyFAH 适用: 人, 小鼠, 大鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (AA 1-419) antibodyFAH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (N-Term) antibodyFAH 适用: 人, 小鼠, 大鼠, 犬, 马, Cow, 豚鼠, Pig WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (AA 2-250) antibodyFAH 适用: 人 WB, IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (N-Term) antibodyFAH 适用: 人, 犬, 马, 猴 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) antibodyFAH 适用: 人, 小鼠, 大鼠 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (AA 311-360) antibodyFAH 适用: 人, 小鼠, 大鼠, 犬, 马, 小鸡 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (AA 1-419) antibodyFAH 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
anti-Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH) (AA 40-195) antibodyFAH 适用: 人 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
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应用备注
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Western blot, 0.25-0.5 μg/mL, Human, Mouse, Rat
Immunohistochemistry(Paraffin-embedded Section), 2-5 μg/mL, Human, Mouse, Rat
Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human
ELISA, 0.1-0.5 μg/mL, -
1. Berube, D., Phaneuf, D., Tanguay, R. M., Gagne, R. Assignment of the fumarylacetoacetate hydrolase gene to chromosome 15q23-15q25. (Abstract) Cytogenet. Cell Genet. 51: 962 only, 1989. 2. Demers, S. I., Phaneuf, D., Tanguay, R. M. Hereditary tyrosinemia type I: strong association with haplotype 6 in French Canadians permits simple carrier detection and prenatal diagnosis. Am. J. Hum. Genet. 55: 327-333, 1994. 3. Grompe, M., Al-Dhalimy, M. Mutations of the fumarylacetoacetate hydrolase gene in four patients with tyrosinemia, type I. Hum. Mutat. 2: 85-93, 1993. -
限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing.
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- FAH (Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH))
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别名
- FAH
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背景
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Synonyms: Deleted in azoospermia-like, DAZ homolog, DAZ-like autosomal, Deleted in azoospermia-like 1, SPGY-like-autosomal, DAZL, DAZH, DAZL1, DAZLA, SPGYLA
Background: Fumarylacetoacetase is an enzyme that in humans is encoded by the FAH gene located on chromosome 15. The FAH gene is thought to be involved in the catabolism of the amino acid phenylalanine in humans. This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT).
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分子量
- 41 kDa
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基因ID
- 2184
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UniProt
- P16930
抗原
-
